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GBE1 Antikörper (Middle Region)
GBE1
Reaktivität: Human, Maus
WB, IF, EIA
Wirt: Kaninchen
Polyclonal
unconjugated
Produktdetails anti-GBE1 Antikörper
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Target
Alle GBE1 Antikörper anzeigen
GBE1
(Glucan (1,4-alpha-), Branching Enzyme 1 (GBE1))
Bindungsspezifität
Alle Epitope für GBE1 Antikörper
AA 534-564, Middle Region
Reaktivität
Alle Reaktivitäten für GBE1 Antikörper
Human, Maus
Wirt
Alle Wirte für GBE1 Antikörper
Kaninchen
Klonalität
Alle Klonalitäten für GBE1 Antikörper
Polyklonal
Konjugat
Alle Konjugate für GBE1 Antikörper
Dieser GBE1 Antikörper ist unkonjugiert
Applikation
Alle Applikationen für GBE1 Antikörper
Western Blotting (WB), Immunofluorescence (IF), Enzyme Immunoassay (EIA)
Spezifität
This antibody recognizes Human and Mouse GBE1 (Center).
Aufreinigung
Protein A column, followed by peptide affinity purification
Immunogen
KLH conjugated synthetic peptide between 534~564 amino acids from the Central region of human GBE1
Isotyp
Ig Fraction
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Anwendungsinformationen
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Applikationshinweise
Optimal working dilution should be determined by the investigator.
Beschränkungen
Nur für Forschungszwecke einsetzbar
Handhabung
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Format
Liquid
Konzentration
0.25 mg/mL
Buffer
PBS containing 0.09 % (W/V) Sodium Azide as preservative
Konservierungsmittel
Sodium azide
Vorsichtsmaßnahmen
This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
Handhabung
Avoid repeated freezing and thawing.
Lagerung
4 °C/-20 °C
Informationen zur Lagerung
Store undiluted at 2-8 °C for one month or (in aliquots) at -20 °C for longer.
Details zu GBE1
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Target
GBE1
(Glucan (1,4-alpha-), Branching Enzyme 1 (GBE1))
Andere Bezeichnung
GBE1 (GBE1 Produkte )
Synonyme
glgBII antikoerper, APBD antikoerper, GBE antikoerper, GSD4 antikoerper, 2310045H19Rik antikoerper, 2810426P10Rik antikoerper, D16Ertd536e antikoerper, 1,4-alpha-glucan branching protein GlgB antikoerper, 1,4-alpha-glucan branching protein antikoerper, glycogen branching protein antikoerper, glycogen branching enzyme antikoerper, 1,4-alpha-glucan-branching protein antikoerper, glycogen branching enzyme; BE; 1,4-alpha-D-glucan:1,4-alpha-D-glucan 6-glucosyl-transferase antikoerper, 1,4-alpha-glucan branching enzyme 1 antikoerper, glucan (1,4-alpha-), branching enzyme 1 antikoerper, glgB antikoerper, ECs4277 antikoerper, SCO7332 antikoerper, Synpcc7942_1085 antikoerper, AZC_4116 antikoerper, Sros_8169 antikoerper, Despr_0975 antikoerper, GBE1 antikoerper, Gbe1 antikoerper
Hintergrund
GBE1 is a glycogen branching enzyme that catalyzes the transfer of alpha-1,4-linked glucosyl units from the outer end of a glycogen chain to an alpha-1,6 position on the same or a neighboring glycogen chain. Branching of the chains is essential to increase the solubility of the glycogen molecule and, consequently, in reducing the osmotic pressure within cells. Highest level of this enzyme are found in liver and muscle. Mutations in this gene are associated with glycogen storage disease IV (also known as Andersen's disease.Synonyms: 1, 4-alpha-glucan-branching enzyme, Brancher enzyme, Glycogen-branching enzyme
Molekulargewicht
80460 Da
Gen-ID
2632
NCBI Accession
NP_000149
Pathways
Cellular Glucan Metabolic Process
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