OPA3 Antikörper
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- Target Alle OPA3 Antikörper anzeigen
- OPA3 (Optic Atrophy 3 (Autosomal Recessive, with Chorea and Spastic Paraplegia) (OPA3))
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Reaktivität
- Human, Maus, Ratte
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Wirt
- Kaninchen
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Klonalität
- Polyklonal
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Konjugat
- Dieser OPA3 Antikörper ist unkonjugiert
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Applikation
- Western Blotting (WB), Immunohistochemistry (IHC)
- Produktmerkmale
- Polyclonal Antibody
- Aufreinigung
- Affinity purification
- Immunogen
- Recombinant fusion protein of human OPA3 (NP_079412.1).
- Isotyp
- IgG
- Top Product
- Discover our top product OPA3 Primärantikörper
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- Applikationshinweise
- WB 1:500-1:2000 IHC 1:50-1:200
- Beschränkungen
- Nur für Forschungszwecke einsetzbar
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- Format
- Liquid
- Konzentration
- 1 mg/mL
- Buffer
- PBS with 0.02 % sodium azide, 50 % glycerol, pH 7.3
- Konservierungsmittel
- Sodium azide
- Vorsichtsmaßnahmen
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- Lagerung
- -20 °C
- Informationen zur Lagerung
- Store at -20°C. Avoid freeze / thaw cycles.
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- Target
- OPA3 (Optic Atrophy 3 (Autosomal Recessive, with Chorea and Spastic Paraplegia) (OPA3))
- Andere Bezeichnung
- OPA3 (OPA3 Produkte)
- Synonyme
- D630048P19Rik antikoerper, Gm1425 antikoerper, Gm472 antikoerper, MGA3 antikoerper, optic atrophy 3 antikoerper, OPA3, outer mitochondrial membrane lipid metabolism regulator antikoerper, opa3 antikoerper, Opa3 antikoerper, OPA3 antikoerper
- Hintergrund
- The mouse ortholog of this protein co-purifies with the mitochondrial inner membrane. Mutations in this gene have been shown to result in 3-methylglutaconic aciduria type III and autosomal dominant optic atrophy and cataract. Multiple transcript variants encoding different isoforms have been found for this gene.
- Molekulargewicht
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Observed_MW: 20 kDa
Calculated_MW: 19 kDa/20 kDa
- Gen-ID
- 80207
- UniProt
- Q9H6K4
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