Medium-Chain Specific Acyl-CoA Dehydrogenase, Mitochondrial Antikörper

Produktnummer ABIN5965186

Produktdetails

Target: Medium-Chain Specific Acyl-CoA Dehydrogenase, Mitochondrial

Reaktivität: Human, Maus, Ratte

Wirt: Kaninchen

Klonalität: Polyklonal

Konjugat: Unkonjugiert

Applikation: Immunofluorescence (IF)

Aufreinigung: Affinity purification

Immunogen: Recombinant fusion protein of human ACADM (NP_000007.1).

Isotyp: IgG

Anwendungsinformationen

Applikationshinweise: IF 1:50-1:200

Beschränkungen: Nur für Forschungszwecke einsetzbar

Handhabung

Format: Liquid

Konzentration: 1 mg/mL

Buffer: PBS with 0.02 % sodium azide, 50 % glycerol, pH 7.3

Konservierungsmittel: Sodium azide

Vorsichtsmaßnahmen: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Lagerung: -20 °C

Informationen zur Lagerung: Store at -20°C. Avoid freeze / thaw cycles.

Antigendetails

Target: Medium-Chain Specific Acyl-CoA Dehydrogenase, Mitochondrial

Andere Bezeichnung: ACADM

Synonyme: ACAD1 antikoerper, MCAD antikoerper, MCADH antikoerper, AU018656 antikoerper, acyl-CoA dehydrogenase medium chain antikoerper, acyl-Coenzyme A dehydrogenase, medium chain antikoerper, acyl-CoA dehydrogenase, C-4 to C-12 straight chain antikoerper, ACADM antikoerper, Acadm antikoerper

Hintergrund: This gene encodes the medium-chain specific (C4 to C12 straight chain) acyl-Coenzyme A dehydrogenase. The homotetramer enzyme catalyzes the initial step of the mitochondrial fatty acid beta-oxidation pathway. Defects in this gene cause medium-chain acyl-CoA dehydrogenase deficiency, a disease characterized by hepatic dysfunction, fasting hypoglycemia, and encephalopathy, which can result in infantile death. Alternatively spliced transcript variants encoding different isoforms have been found for this gene.

Molekulargewicht:

Observed_MW: 47kDa

Calculated_MW: 46kDa/47kDa

Gen-ID: 34

UniProt: P11310