BCKDHB Antikörper (AA 183-392)

Produktnummer ABIN6137489

Produktdetails anti-BCKDHB Antikörper

Target: BCKDHB (Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB))

Bindungsspezifität: AA 183-392

Reaktivität: Human

Wirt: Kaninchen

Klonalität: Polyklonal

Konjugat: Dieser BCKDHB Antikörper ist unkonjugiert

Applikation: Western Blotting (WB)

Sequenz: RSPWGCVGHG ALYHSQSPEA FFAHCPGIKV VIPRSPFQAK GLLLSCIEDK NPCIFFEPKI LYRAAAEEVP IEPYNIPLSQ AEVIQEGSDV TLVAWGTQVH VIREVASMAK EKLGVSCEVI DLRTIIPWDV DTICKSVIKT GRLLISHEAP LTGGFASEIS STVQEECFLN LEAPISRVCG YDTPFPHIFE PFYIPDKWKC YDALRKMINY

Kreuzreaktivität: Maus

Produktmerkmale: Polyclonal Antibodies

Aufreinigung: Affinity purification

Immunogen: Recombinant fusion protein containing a sequence corresponding to amino acids 183-392 of human BCKDHB (NP_898871.1).

Isotyp: IgG

Anwendungsinformationen

Applikationshinweise: WB,1:500 - 1:2000

Beschränkungen: Nur für Forschungszwecke einsetzbar

Handhabung

Format: Liquid

Buffer: PBS with 0.02 % sodium azide,50 % glycerol, pH 7.3.

Konservierungsmittel: Sodium azide

Vorsichtsmaßnahmen: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Lagerung: -20 °C

Informationen zur Lagerung: Store at -20°C. Avoid freeze / thaw cycles.

Details zu BCKDHB

Target: BCKDHB (Branched Chain Keto Acid Dehydrogenase E1, beta Polypeptide (BCKDHB))

Andere Bezeichnung: BCKDHB (BCKDHB Produkte)

Synonyme: zgc:158777 antikoerper, BCKDHB antikoerper, E1B antikoerper, dJ279A18.1 antikoerper, branched chain keto acid dehydrogenase E1, beta polypeptide antikoerper, branched chain keto acid dehydrogenase E1 subunit beta antikoerper, branched chain keto acid dehydrogenase E1, beta polypeptide S homeolog antikoerper, branched chain ketoacid dehydrogenase E1, beta polypeptide antikoerper, BCKDHB antikoerper, bckdhb antikoerper, bckdhb.S antikoerper, Bckdhb antikoerper

Hintergrund: This gene encodes the E1 beta subunit of branched-chain keto acid dehydrogenase, which is a multienzyme complex associated with the inner membrane of mitochondria. This enzyme complex functions in the catabolism of branched-chain amino acids. Mutations in this gene have been associated with maple syrup urine disease (MSUD), type 1B, a disease characterized by a maple syrup odor to the urine in addition to mental and physical retardation and feeding problems. Alternative splicing at this locus results in multiple transcript variants.,BCKDHB,BCKDE1B,BCKDH E1-beta,E1B,BCKDHE1-beta,Cancer,Signal Transduction,Endocrine & Metabolism,Mitochondrial metabolism,Mitochondrial markers,Amino acid metabolism,BCKDHB

Molekulargewicht: 23 kDa/43 kDa

Gen-ID: 594

UniProt: P21953