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ALDH5A1 Antikörper (Internal Region)
ALDH5A1
Reaktivität: Human, Ratte, Maus, Rind (Kuh), Hund
WB, EIA
Wirt: Ziege
Polyclonal
unconjugated
Produktdetails anti-ALDH5A1 Antikörper
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Target
Alle ALDH5A1 Antikörper anzeigen
ALDH5A1
(Aldehyde Dehydrogenase 5 Family, Member A1 (ALDH5A1))
Bindungsspezifität
Alle Epitope für ALDH5A1 Antikörper
AA 301-312, Internal Region
Reaktivität
Alle Reaktivitäten für ALDH5A1 Antikörper
Human, Ratte, Maus, Rind (Kuh), Hund
Wirt
Alle Wirte für ALDH5A1 Antikörper
Ziege
Klonalität
Alle Klonalitäten für ALDH5A1 Antikörper
Polyklonal
Konjugat
Alle Konjugate für ALDH5A1 Antikörper
Dieser ALDH5A1 Antikörper ist unkonjugiert
Applikation
Alle Applikationen für ALDH5A1 Antikörper
Western Blotting (WB), Enzyme Immunoassay (EIA)
Sequenz
C-TGKILLHHAA NS
Spezifität
This antibody is expected to recognize both reported isoforms (NP_733936.1, NP_001071.1).
Kreuzreaktivität (Details)
Species reactivity (expected):Canine (Dog), Bovine. Species reactivity (tested):Human, Mouse, Rat.
Aufreinigung
Ammonium Sulphate Precipitation followed by antigen Affinity Chromatography using the immunizing peptide
Immunogen
Peptide with sequence from the internal region of the protein sequence according to NP_733936.1 NP_001071.1.
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Anwendungsinformationen
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Applikationshinweise
Optimal working dilution should be determined by the investigator.
Beschränkungen
Nur für Forschungszwecke einsetzbar
Handhabung
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Konzentration
0.5 mg/mL
Buffer
Tris saline, pH ~7.3 with 0.02 % Sodium Azide and 0.5 % BSA
Konservierungsmittel
Sodium azide
Vorsichtsmaßnahmen
This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
Handhabung
Avoid repeated freezing and thawing.
Lagerung
4 °C/-20 °C
Informationen zur Lagerung
Store the antibody undiluted at 2-8 °C for one month or (in aliquots) at -20 °C for longer.
Details zu ALDH5A1
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Target
ALDH5A1
(Aldehyde Dehydrogenase 5 Family, Member A1 (ALDH5A1))
Andere Bezeichnung
ALDH5A1 / SSADH (ALDH5A1 Produkte )
Synonyme
SSADH antikoerper, SSDH antikoerper, Ssadh antikoerper, 6330403E24Rik antikoerper, Ahd-1 antikoerper, Ahd1 antikoerper, D630032B01Rik antikoerper, OTTMUSG00000000613 antikoerper, Ssdh1 antikoerper, aldehyde dehydrogenase 5 family member A1 antikoerper, aldehyde dehydrogenase 5 family, member A1 antikoerper, aldhehyde dehydrogenase family 5, subfamily A1 antikoerper, ALDH5A1 antikoerper, aldh5a1 antikoerper, Aldh5a1 antikoerper
Hintergrund
Defects in ALDH5A1 are the cause of succinate semialdehyde dehydrogenase deficiency (SSADH deficiency) [MIM:271980]. SSADH deficiency is a rare inborn error in the metabolism of 4-aminobutyric acid (GABA) which leads to accumulation of 4-hydroxybutyric acid in physiologic fluids of patients. The disease is characterized by severe ataxia and by mildly retarded psychomotor development.Synonyms: Aldehyde dehydrogenase family 5 member A1, NAD(+)-dependent succinic semialdehyde dehydrogenase, Succinate-semialdehyde dehydrogenase, mitochondrial
Molekulargewicht
58.7kDa (NP_733936.1).
Gen-ID
7915
NCBI Accession
NP_001071
UniProt
P51649
Pathways
Monocarboxylic Acid Catabolic Process
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