HADHA Antikörper (Middle Region)

Produktnummer ABIN5516771

Produktdetails anti-HADHA Antikörper

Target: HADHA (Hydroxyacyl-Coenzyme A Dehydrogenase/3-Ketoacyl-Coenzyme A Thiolase/enoyl-Coenzyme A Hydratase (Trifunctional Protein), alpha Subunit (HADHA))

Bindungsspezifität: Middle Region

Reaktivität: Human

Wirt: Kaninchen

Klonalität: Polyklonal

Konjugat: Dieser HADHA Antikörper ist unkonjugiert

Applikation: Western Blotting (WB)

Sequenz: IYQEGVKRKD LNSDMDSILA SLKLPPKSEV SSDEDIQFRL VTRFVNEAVM

Aufreinigung: Affinity purified

Immunogen: The immunogen is a synthetic peptide directed towards the middle region of human HADHA

Anwendungsinformationen

Applikationshinweise: Optimal working dilution should be determined by the investigator.

Beschränkungen: Nur für Forschungszwecke einsetzbar

Handhabung

Format: Liquid

Buffer: Liquid. Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.

Konservierungsmittel: Sodium azide

Vorsichtsmaßnahmen: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Lagerung: -20 °C

Informationen zur Lagerung: For short term use, store at 2-8°C up to 1 week. For long term storage, store at -20°C in small aliquots to prevent freeze-thaw cycles.

Details zu HADHA

Target: HADHA (Hydroxyacyl-Coenzyme A Dehydrogenase/3-Ketoacyl-Coenzyme A Thiolase/enoyl-Coenzyme A Hydratase (Trifunctional Protein), alpha Subunit (HADHA))

Andere Bezeichnung: HADHA (HADHA Produkte)

Synonyme: cb1055 antikoerper, hadha antikoerper, im:7136067 antikoerper, wu:fa14c08 antikoerper, ECHA antikoerper, GBP antikoerper, HADH antikoerper, LCEH antikoerper, LCHAD antikoerper, MTPA antikoerper, TP-ALPHA antikoerper, RGD1560655 antikoerper, C77020 antikoerper, Mtpa antikoerper, hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha antikoerper, hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), alpha subunit antikoerper, hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha S homeolog antikoerper, hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alpha a antikoerper, hydroxyacyl-Coenzyme A dehydrogenase/3-ketoacyl-Coenzyme A thiolase/enoyl-Coenzyme A hydratase (trifunctional protein), alpha subunit antikoerper, HADHA antikoerper, hadha antikoerper, hadha.S antikoerper, hadhaa antikoerper, Hadha antikoerper

Hintergrund: This gene encodes the alpha subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits, with the alpha subunit catalyzing the 3-hydroxyacyl-CoA dehydrogenase and enoyl-CoA hydratase activities. Mutations in this gene result in trifunctional protein deficiency or LCHAD deficiency. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation.

Alias Symbols: GBP, ECHA, HADH, LCEH, MTPA, LCHAD, TP-ALPHA

Protein Size: 763

Gen-ID: 3030

NCBI Accession: NM_000182, NP_000173

UniProt: P40939

Pathways: Monocarboxylic Acid Catabolic Process