anti-Succinate-CoA Ligase, alpha Subunit (SUCLG1) Antikörper

SUCLG1 encodes the alpha subunit of the heterodimeric enzyme succinate coenzyme A ligase. Zusätzlich bieten wir Ihnen Succinate-CoA Ligase, alpha Subunit Proteine (7) und viele weitere Produktgruppen zu diesem Protein an.

Alle Antikörper anzeigen Gen GeneID UniProt
SUCLG1 8802 P53597
SUCLG1 114597 P13086
SUCLG1 56451 Q9WUM5
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Top anti-Succinate-CoA Ligase, alpha Subunit Antikörper auf antikoerper-online.de

Showing 10 out of 24 products:

Katalog Nr. Reaktivität Wirt Konjugat Applikation Bilder Menge Anbieter Lieferzeit Preis Details
Rind (Kuh) Kaninchen Unkonjugiert WB 100 μL Anmelden zum Anzeigen 6 bis 8 Tage
358,51 €
Details
Rind (Kuh) Kaninchen Unkonjugiert WB 100 μL Anmelden zum Anzeigen 6 bis 8 Tage
358,51 €
Details
Human Kaninchen Unkonjugiert ICC, IF, IHC, IHC (p), IP, WB Western Blot: SUCLG1 Antibody [NBP1-32728] - Sample (30 ug of whole cell lysate) A: A431 10% SDS PAGE, antibody diluted at 1:1000. Immunocytochemistry/Immunofluorescence: SUCLG1 Antibody [NBP1-32728] - Sample: HeLa cells were fixed in 2% paraformaldehyde/culture medium at 37C for 30 min. Green: SUCLG1 protein stained by SUCLG1 antibody diluted at 1:500. Blue: Hoechst 33342 staining. 100 μL Anmelden zum Anzeigen 2 bis 4 Tage
341,00 €
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Schwein Kaninchen Biotin DB, EIA, ID, IF, IP, RIA, WB   1 mL Anmelden zum Anzeigen 7 bis 9 Tage
385,00 €
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Human Kaninchen Unkonjugiert ICC, IF, IHC (p), WB ICC/IF Image SUCLG1 antibody detects SUCLG1 protein at mitochondria by confocal immunofluorescent analysis. Sample: HeLa cells were fixed in 2% paraformaldehyde/culture medium at 37℃ for 30 min. Green: SUCLG1 protein stained by SUCLG1 antibody , diluted at 1:500. Blue: Hoechst 33342 staining. [Images captured by Olympus FV10i Confocal Laser Scanning Microscope] IHC-P Image Immunohistochemical analysis of paraffin-embedded N87 xenograft, using SUCLG1, antibody at 1:100 dilution. 100 μL Anmelden zum Anzeigen 5 bis 7 Tage
357,24 €
Details
Rind (Kuh) Kaninchen Unkonjugiert WB   50 μg Anmelden zum Anzeigen 11 bis 14 Tage
653,02 €
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Fledermaus Kaninchen Unkonjugiert WB   50 μg Anmelden zum Anzeigen 11 bis 14 Tage
653,02 €
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Schwein Kaninchen Unkonjugiert DB, EIA, ID, IF, IP, RIA, WB   10 mg Anmelden zum Anzeigen 7 bis 9 Tage
264,00 €
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Human Kaninchen Unkonjugiert WB   50 μL Anmelden zum Anzeigen 11 bis 14 Tage
548,26 €
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Human Kaninchen Unkonjugiert IP, WB   100 μL Anmelden zum Anzeigen 11 bis 14 Tage
827,62 €
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SUCLG1 Antikörper nach Reaktivität, Anwendung, Klonalität and Konjugat

Attribute Applikationen Wirt Klonalität
Human
,

Rat (Rattus)


Mouse (Murine)


Weitere Antikörper gegen Succinate-CoA Ligase, alpha Subunit Interaktionspartner

Human Succinate-CoA Ligase, alpha Subunit (SUCLG1) Interaktionspartner

  1. Long survival, to age 20 years or older, was reported in 12% of SUCLA2 (zeige SUCLA2 Antikörper) and in 10% of SUCLG1 patients.

  2. First Chinese report of succinyl-CoA ligase (zeige SUCLG2 Antikörper) deficiency caused by novel SUCLG1 mutations; five novel pathogenic mutations in SUCLG1 were identified

  3. 3 novel mutations have been identified in patients with the mitochondrial DNA depletion syndrome (c.1048G>A and c.1049G>T in SUCLA2 (zeige SUCLA2 Antikörper) and c.531+4A>T in SUCLG1).

  4. Our results suggest that SUCLG1 mutations that lead to complete absence of SUCLG1 protein are responsible for a very severe disorder with antenatal manifestations, whereas a SUCLA2 (zeige SUCLA2 Antikörper)-like phenotype is found in patients with residual SUCLG1 protein.

  5. This report enlarges the phenotypic spectrum of SUCLG1 mutations and confirms that a characteristic metabolic profile (presence of MMA and C4-DC carnitine in urines) and basal ganglia MRI (zeige C7ORF49 Antikörper) lesions are the hallmarks of SCS (zeige TWIST1 Antikörper) defects.

  6. A novel mutation in the SUCLG1 gene was found in two newborns having lethal lactic acidosis, multi-organ failure and congenital malformations including interrupted aortic arch.

Pig (Porcine) Succinate-CoA Ligase, alpha Subunit (SUCLG1) Interaktionspartner

  1. Structure of GTP-specific succinyl-CoA synthetase subunits in complex with CoA has been resolved.

  2. succinyl-CoA (zeige OXCT1 Antikörper) synthetase is able to protect GTP (zeige AK3 Antikörper) from hydrolysis when the active-site histidine residue is not in position to be phosphorylated

Mouse (Murine) Succinate-CoA Ligase, alpha Subunit (SUCLG1) Interaktionspartner

  1. ADP and GDP succinyl-CoA (zeige OXCT1 Antikörper) synthetases have different expression patterns and specificity

Succinate-CoA Ligase, alpha Subunit (SUCLG1) Antigen-Profil

Protein Überblick

This gene encodes the alpha subunit of the heterodimeric enzyme succinate coenzyme A ligase. This enzyme is targeted to the mitochondria and catalyzes the conversion of succinyl CoA and ADP or GDP to succinate and ATP or GTP. Mutations in this gene are the cause of the metabolic disorder fatal infantile lactic acidosis and mitochondrial DNA depletion.

Genbezeichner und Symbole assoziert mit SUCLG1

  • succinate-CoA ligase, alpha subunit (SUCLG1) Antikörper
  • succinate-CoA ligase, alpha subunit (suclg1) Antikörper
  • succinate-CoA ligase, alpha subunit (Suclg1) Antikörper
  • succinate-CoA ligase, GDP-forming, alpha subunit (suclg1) Antikörper
  • succinate-CoA ligase, GDP-forming, alpha subunit (Suclg1) Antikörper
  • 1500000I01Rik Antikörper
  • GALPHA Antikörper
  • MTDPS9 Antikörper
  • SCS Antikörper
  • Sucla1 Antikörper
  • zgc:92738 Antikörper
  • zgc:103729 Antikörper

Bezeichner auf Proteinebene für SUCLG1

succinate-CoA ligase, GDP-forming, alpha subunit , succinate-CoA ligase, GDP-forming alpha subunit , SCS-alpha , succinyl-CoA ligase [ADP/GDP-forming] subunit alpha, mitochondrial , succinyl-CoA ligase [GDP-forming] subunit alpha, mitochondrial , succinyl-CoA synthetase subunit alpha , succinyl-CoA synthetase alpha subunit , SUCLGa

GENE ID SPEZIES
470417 Pan troglodytes
475775 Canis lupus familiaris
494796 Xenopus laevis
594977 Xenopus (Silurana) tropicalis
8802 Homo sapiens
399539 Sus scrofa
114597 Rattus norvegicus
509983 Bos taurus
436850 Danio rerio
56451 Mus musculus
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