anti-Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit (HADHB) Antikörper

Bezeichnung:
anti-Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit Antikörper (HADHB)
Auf www.antikoerper-online.de finden Sie aktuell 74 Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit (HADHB) Antikörper von 15 unterschiedlichen Herstellern. Zusätzlich bieten wir Ihnen Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit Proteine (13) und Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit Kits (9) und viele weitere Produktgruppen zu diesem Protein an. Insgesamt sind aktuell 103 Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit Produkte verfügbar.
Synonyme:
4930479F15Rik, ECHB, fb14g10, Hadhb, Mtpb, thiolase, TP-BETA, wu:fb14g10, zgc:56274

Meistgesuchte Reaktivitäten zu anti-Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit (HADHB) Antikörper

Wählen Sie die Spezies und Applikation aus

anti-Human Antikörper:

anti-Rat (Rattus) Antikörper:

anti-Mouse (Murine) Antikörper:

Alle verfügbaren anti-Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit Antikörper

Sie gelangen zu unserer vorgefilterten Suche.

Am meisten referenzierte anti-Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit Antikörper

  1. Cow (Bovine) Polyclonal HADHB Primary Antibody für IHC, WB - ABIN2783232 : Wang, Yang, Zhu, Wang, Yang, Wang, Zhai, Li, Yu: [Screening for G1528C mutation in mitochondrial trifunctional protein gene in pregnant women with severe preeclampsia and new born infant]. in Zhonghua fu chan ke za zhi 2007 (PubMed)
    Zeige alle 3 Referenzen für 2783232

  2. Human Polyclonal HADHB Primary Antibody für EIA, FACS - ABIN952676 : Purevsuren, Fukao, Hasegawa, Kobayashi, Li, Mushimoto, Fukuda, Yamaguchi: Clinical and molecular aspects of Japanese patients with mitochondrial trifunctional protein deficiency. in Molecular genetics and metabolism 2009 (PubMed)
    Zeige alle 3 Referenzen für 952676

Weitere Antikörper gegen Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit Interaktionspartner

Human Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit (HADHB) Interaktionspartner

  1. Exposure to bezafibrate (400 muM for 48 h) increased the abundance of HADHA (zeige HADHA Antikörper) and HADHB mRNAs.

  2. nonstructural protein 5 (zeige CAPS Antikörper) (NS5 (zeige RAF1 Antikörper)) interacted with hydroxyacyl-CoA dehydrogenase (zeige HADH Antikörper) alpha and beta subunits, two components of the mitochondrial trifunctional protein (MTP) involved in LCFA beta-oxidation

  3. Mutations in HADHB, which encodes the beta-subunit of mitochondrial trifunctional protein, cause infantile onset hypoparathyroidism and peripheral polyneuropathy.

  4. Heterozygous mutation in HADHB gene cause early-onset axonal axonal Charcot-Marie-tooth disease.

  5. The results demonstrated that ERbeta (zeige ESR2 Antikörper) was indeed associated and colocalized with HADHB within mitochondria.

  6. HADHB is a functional molecular target of estrogen receptor alpha (zeige ESR1 Antikörper) in the mitochondria, and the interaction may play an important role in the estrogen-mediated lipid metabolism in animals and humans.

  7. mutational analysis of the HADHB gene, which encodes long-chain 3-ketoacyl-CoA thiolase, identified compound heterozygous mutations of c.520C>T (p.R141C) and c.1331G>A (p.R411K) in a case of mitochondrial trifunctional protein deficiency

  8. Results emphasize the value of cDNA analysis in the characterization of HADHA (zeige HADHA Antikörper) and HADHB mutations and further strengthen the model of haploinsufficiency as a major pathomechanism in MTP defects.

  9. Recombinant mitochondrial trifunctional protein displayed 2-enoyl-CoA hydratase, l-3-hydroxyacyl-CoA dehydrogenase, and 3-ketoacyl-CoA thiolase activities.

  10. The present findings showed that all missense mutations in HADHB were disease-causing.

Cow (Bovine) Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit (HADHB) Interaktionspartner

  1. Mutation analysis of the HADHB gene of patient 4 identified compound heterozygosity of N114D/N307D.

Mouse (Murine) Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit (HADHB) Interaktionspartner

  1. nonstructural protein 5 (zeige CAPS Antikörper) (NS5 (zeige RAF1 Antikörper)) interacted with hydroxyacyl-CoA dehydrogenase (zeige HADH Antikörper) alpha and beta subunits, two components of the mitochondrial trifunctional protein (MTP (zeige LAPTM4A Antikörper)) involved in LCFA beta-oxidation

Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit (HADHB) Antigen-Profil

Beschreibung des Gens

This gene encodes the beta subunit of the mitochondrial trifunctional protein, which catalyzes the last three steps of mitochondrial beta-oxidation of long chain fatty acids. The mitochondrial membrane-bound heterocomplex is composed of four alpha and four beta subunits, with the beta subunit catalyzing the 3-ketoacyl-CoA thiolase activity. Mutations in this gene result in trifunctional protein deficiency. The encoded protein can also bind RNA and decreases the stability of some mRNAs. The genes of the alpha and beta subunits of the mitochondrial trifunctional protein are located adjacent to each other in the human genome in a head-to-head orientation. Alternatively spliced transcript variants have been found\; however, their full-length nature is not known.

Alternative names and synonyms associated with Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit (HADHB)

  • hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), beta subunit (HADHB) Antikörper
  • hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), beta subunit (hadhb) Antikörper
  • hydroxyacyl-CoA dehydrogenase/3-ketoacyl-CoA thiolase/enoyl-CoA hydratase (trifunctional protein), beta subunit (Hadhb) Antikörper
  • hydroxyacyl-Coenzyme A dehydrogenase/3-ketoacyl-Coenzyme A thiolase/enoyl-Coenzyme A hydratase (trifunctional protein), beta subunit (hadhb) Antikörper
  • hydroxyacyl-Coenzyme A dehydrogenase/3-ketoacyl-Coenzyme A thiolase/enoyl-Coenzyme A hydratase (trifunctional protein), beta subunit (Hadhb) Antikörper
  • long-chain 3-ketoacyl-CoA thiolase (LCTHIO) Antikörper
  • 4930479F15Rik Antikörper
  • ECHB Antikörper
  • fb14g10 Antikörper
  • Hadhb Antikörper
  • Mtpb Antikörper
  • thiolase Antikörper
  • TP-BETA Antikörper
  • wu:fb14g10 Antikörper
  • zgc:56274 Antikörper

Bezeichner auf Proteinebene für HADHB

2-enoyl-Coenzyme A (CoA) hydratase, beta subunit , 3-ketoacyl-Coenzyme A (CoA) thiolase of mitochondrial trifunctional protein, beta subunit , acetyl-CoA acyltransferase , beta-ketothiolase , hydroxyacyl-Coenzyme A dehydrogenase/3-ketoacyl-Coenzyme A thiolase/enoyl-Coenzyme A hydratase (trifunctional protein), beta subunit , trifunctional enzyme subunit beta, mitochondrial , hydroxyacyl dehydrogenase, subunit B , TP-beta , dehydrogenase/3-ketoacyl-Coenzyme A thiolase/enoyl-Coenzyme A hydratase (trifunctional protein), beta subunit , mitochondrial trifunctional protein, beta subunit , 3-ketoacyl-Coenzyme A thiolase , TP-Beta , enoyl-Coenzyme A hydratase, beta subunit , trifunctional enzyme beta subunit, mitochondrial , dehydrogenase/3-ketoacyl-Coenzyme A thiolase , hydroxyacyl-Coenzyme A dehydrogenase/3-ketoacyl-Coenzyme A thiolase/enoyl-Coenzyme A hydratase (trifunctional protein), beta aubunit

GENE ID SPEZIES
3032 Homo sapiens
379769 Xenopus laevis
421995 Gallus gallus
281811 Bos taurus
171155 Rattus norvegicus
607926 Canis lupus familiaris
459080 Pan troglodytes
336606 Danio rerio
231086 Mus musculus
397017 Sus scrofa
Ausgewählte Anbieter für anti-Hydroxyacyl-CoA Dehydrogenase/3-Ketoacyl-CoA Thiolase/enoyl-CoA Hydratase (Trifunctional Protein), beta Subunit (HADHB) Antikörper
Haben Sie etwas anderes gesucht?