AMMECR1 Antikörper (C-Term)
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- Target Alle AMMECR1 Antikörper anzeigen
- AMMECR1 (Alport Syndrome, Mental Retardation, Midface Hypoplasia and Elliptocytosis Chromosomal Region Gene 1 (AMMECR1))
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Bindungsspezifität
- AA 271-298, C-Term
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Reaktivität
- Human
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Wirt
- Kaninchen
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Klonalität
- Polyklonal
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Konjugat
- Dieser AMMECR1 Antikörper ist unkonjugiert
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Applikation
- Western Blotting (WB)
- Homologie
- M
- Aufreinigung
- This antibody is purified through a protein A column, followed by peptide affinity purification.
- Immunogen
- This AMMECR1 antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide between 271-298 amino acids from the C-terminal region of human AMMECR1.
- Klon
- RB39848
- Isotyp
- Ig Fraction
- Top Product
- Discover our top product AMMECR1 Primärantikörper
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- Applikationshinweise
- WB: 1:1000
- Beschränkungen
- Nur für Forschungszwecke einsetzbar
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- Format
- Liquid
- Buffer
- Purified polyclonal antibody supplied in PBS with 0.09 % (W/V) sodium azide.
- Konservierungsmittel
- Sodium azide
- Vorsichtsmaßnahmen
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
- Lagerung
- 4 °C,-20 °C
- Informationen zur Lagerung
- AMMECR1 Antibody (C-term) can be refrigerated at 2-8 °C for up to 6 months. For long term storage, keep at -20 °C.
- Haltbarkeit
- 6 months
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- Target
- AMMECR1 (Alport Syndrome, Mental Retardation, Midface Hypoplasia and Elliptocytosis Chromosomal Region Gene 1 (AMMECR1))
- Andere Bezeichnung
- AMMECR1 (AMMECR1 Produkte)
- Synonyme
- ammerc1 antikoerper, MGC84095 antikoerper, AMMECR1 antikoerper, Ammecr1 antikoerper, AMMERC1 antikoerper, 6230420G18Rik antikoerper, Alport syndrome, mental retardation, midface hypoplasia and elliptocytosis chromosomal region gene 1 L homeolog antikoerper, Alport syndrome, mental retardation, midface hypoplasia and elliptocytosis chromosomal region gene 1 antikoerper, ammecr1.L antikoerper, AMMECR1 antikoerper, Ammecr1 antikoerper, ammecr1 antikoerper
- Hintergrund
- The exact function of this gene is not known, however, submicroscopic deletion of the X chromosome including this gene, COL4A5, and FACL4 genes, result in a contiguous gene deletion syndrome, the AMME complex (Alport syndrome, mental retardation, midface hypoplasia, and elliptocytosis). Alternatively spliced transcript variants encoding different isoforms have been found for this gene.
- Molekulargewicht
- 35463
- Gen-ID
- 9949
- NCBI Accession
- NP_001020751, NP_001165160, NP_056180
- UniProt
- Q9Y4X0
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