Galactosidase, alpha (GLA) ELISA Kits

GLA encodes a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. Zusätzlich bieten wir Ihnen GLA Antikörper (129) und GLA Proteine (18) und viele weitere Produktgruppen zu diesem Protein an.

list all ELISA KIts Gen GeneID UniProt
GLA 2717 P06280
GLA 11605  
Anti-Ratte GLA GLA 363494  
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Top GLA ELISA Kits auf antikoerper-online.de

Showing 10 out of 37 products:

Katalog Nr. Reaktivität Sensitivität Bereich Bilder Menge Anbieter Lieferzeit Preis Details
Human 0.062 ng/mL 0.156-10 ng/mL 96 Tests Anmelden zum Anzeigen 15 bis 17 Tage
$832.83
Details
Maus 7.81   96 Tests Anmelden zum Anzeigen 15 bis 18 Tage
$910.56
Details
Human 0.04 ng/mL 0.156-10 ng/mL   96 Tests Anmelden zum Anzeigen 2 bis 3 Tage
$713.90
Details
Meerschweinchen
  96 Tests Anmelden zum Anzeigen 15 bis 18 Tage
$707.14
Details
Schwein 46.875 pg/mL 78.125-5000 pg/mL   96 Tests Anmelden zum Anzeigen 12 bis 14 Tage
$715.00
Details
Huhn 2.344 pg/mL 3.906-250 pg/mL   96 Tests Anmelden zum Anzeigen 12 bis 14 Tage
$715.00
Details
Kaninchen 1.875 pg/mL 3.125-200 pg/mL   96 Tests Anmelden zum Anzeigen 12 bis 14 Tage
$715.00
Details
Affe 46.875 pg/mL 78.125-5000 pg/mL   96 Tests Anmelden zum Anzeigen 12 bis 14 Tage
$715.00
Details
Rind (Kuh)
  96 Tests Anmelden zum Anzeigen 15 bis 18 Tage
$707.14
Details
Schaf
  96 Tests Anmelden zum Anzeigen 15 bis 18 Tage
$707.14
Details

Weitere ELISA Kits für GLA Interaktionspartner

Human Galactosidase, alpha (GLA) Interaktionspartner

  1. Four patients had non-amenable mutant forms of a-Gal (zeige GAL ELISA Kits) based on the validated cell-based assay conducted after treatment initiation and were excluded from primary efficacy analyses only.

  2. Mesenchymal stem cells with reduced GLA (zeige NAT8 ELISA Kits) activity are prone to apoptosis and senescence due to impaired autophagy and DNA repair capacity.

  3. we review the various types of GLA (zeige NAT8 ELISA Kits) variants and recommend that pathogenicity be considered only when associated with elevated globotriaosylceramide in disease-relevant organs and tissues as analyzed by mass spectrometry.

  4. findings revealed the alternative splicing mechanism of GLA (zeige NAT8 ELISA Kits) (IVS4+919G>A), and a potential treatment for this specific genetic type of Fabry disease by amiloride in the future

  5. Results found a novel heterozygous stop codon mutation in exon 1 of the GLA (zeige NAT8 ELISA Kits) gene in female patients with Fabry Disease with methylation in the non-mutated allele thought to be associated with the clinical severity of the disease.

  6. Study described the demographic data, wide clinical spectrum of phenotypes, and GLA (zeige NAT8 ELISA Kits) mutation spectrum of Fabry disease in Korea. Most of the patients had classical Fabry disease, with a 4 times higher incidence than that of late-onset Fabry disease, indicating an underdiagnosis of mild, late-onset Fabry disease.

  7. we reviewed other small molecules that were reported to have a stabilizing effect on some GLA (zeige NAT8 ELISA Kits) missense mutations in vitro and might be developed to act in synergy or as an alternative to 1-deoxygalactonojirimycin

  8. No pathogenic mutations in the coding regions of the GLA (zeige NAT8 ELISA Kits) gene were identified in this group of patients and thus no Fabry disease was found in this study.

  9. High desphospho-uncarboxylated matrix Gla protein (zeige MGP ELISA Kits) level, reflecting a poor vitamin K status, seems to be associated with kidney damage and may be also a marker of cardiovascular risk in CKD patients

  10. Case Report: Kidney transplantation from a mother with unrecognized Fabry disease to her son with low alpha-galactosidase A activity.

Mouse (Murine) Galactosidase, alpha (GLA) Interaktionspartner

  1. the GM130 (zeige GOLGA2 ELISA Kits)-deficient mouse provides a valuable model for investigating the etiology of human globozoospermia.

  2. Mice with alpha-galactosidase A deficiency show age-dependent and distinct deficits of the sensory system.

  3. In oocyte meiosis, GM130 (zeige GOLGA2 ELISA Kits) localization and expression patterns are regulated by FMNL1 (zeige FMNL1 ELISA Kits).

  4. The histological changes in Gla KO mice better resemble the type 2 later-onset phenotype observed in patients with residual alpha-galactosidase A activity.

  5. our findings imply that the alpha-GalA KO mouse is a good model in which to study the peripheral small fiber neuropathy exhibited by FD patients

  6. we demonstrate an age-dependent microvasculopathy of the mesenteric artery in a murine model of Fabry disease (galactosidase A-knockout mice) resulting from dysregulation of the vascular homeostatic enzyme endothelial nitric oxide synthase (eNOS (zeige NOS3 ELISA Kits))

  7. GM130 (zeige GOLGA2 ELISA Kits) regulates microtubule organization and might cooperate with the MAPK (zeige MAPK1 ELISA Kits) pathway to play roles in spindle organization, migration and asymmetric division during mouse oocyte maturation

  8. It suggested that there could be a combination of GLA deficiency and FVL (zeige F5 ELISA Kits) or other thrombosis-related gene defect in patients with genetic severe early-onset thrombosis.

  9. present Toll (zeige TLR4 ELISA Kits)-like receptor-dependent negative regulation of alpha-Gal-A as a mechanistic link between pathogen recognition and self lipid antigen induction for natural killer T cells

  10. Developed a novel recombinant lentiviral vector that engineers expression of alpha-galactosidase. Analysis of tissues at 26 wks demonstrated similar alpha-gal A enzyme activities but enhanced Gb3 reduction in hearts and kidneys compared with control.

GLA Antigen-Profil

Beschreibung des Gens

This gene encodes a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties.

Genbezeichner und Symbole assoziert mit Galactosidase, alpha (GLA) ELISA Kits

  • galactosidase alpha (GLA) Antikörper
  • galactosidase, alpha (Gla) Antikörper
  • galactosidase, alpha (gla) Antikörper
  • galactosidase alpha S homeolog (gla.S) Antikörper
  • galactosidase alpha (gla) Antikörper
  • alpha-galactosidase (agaN) Antikörper
  • aga (aga) Antikörper
  • alpha-galactosidase (agaL) Antikörper
  • alpha-galactosidase (SCO0541) Antikörper
  • alpha-galactosidase (rafA) Antikörper
  • alpha-galactosidase (melA) Antikörper
  • alpha-galactosidase (galA) Antikörper
  • alpha-galactosidase A (ANI_1_2528074) Antikörper
  • alpha-galactosidase A (ANI_1_1502124) Antikörper
  • alpha-galactosidase A (AOR_1_390174) Antikörper
  • alpha-galactosidase A (CpipJ_CPIJ002066) Antikörper
  • alpha-galactosidase (aga) Antikörper
  • alpha-galactosidase A (MCYG_00962) Antikörper
  • alpha-galactosidase A (MCYG_00791) Antikörper
  • alpha-galactosidase (gla) Antikörper
  • alpha-galactosidase A (Tsp_02909) Antikörper
  • alpha-galactosidase A (Tsp_02508) Antikörper
  • golgi autoantigen, golgin subfamily a, 2 (Golga2) Antikörper
  • galactosidase alpha (Gla) Antikörper
  • galactosidase, alpha (GLA) Antikörper
  • Ags Antikörper
  • alpha-GAL Antikörper
  • AO090005000217 Antikörper
  • AW555139 Antikörper
  • GALA Antikörper
  • GM130 Antikörper
  • MGC130872 Antikörper
  • mKIAA4150 Antikörper
  • SCF11.21 Antikörper
  • SMU.877 Antikörper
  • zgc:101584 Antikörper

Bezeichner auf Proteinebene für Galactosidase, alpha (GLA) ELISA Kits

agalsidase alfa , alpha-D-galactosidase A , alpha-D-galactoside galactohydrolase 1 , alpha-gal A , alpha-galactosidase A , melibiase , alpha-D-galactoside galactohydrolase , Alpha-galactosidase A , galactosidase, alpha , alpha-galactosidase A-like , alpha-galactosidase , Alpha-galactosidase , 130 kDa cis-Golgi matrix protein , Golgin subfamily A member 2 , SY11 protein , golgin-95

GENE ID SPEZIES
2717 Homo sapiens
11605 Mus musculus
363494 Rattus norvegicus
422188 Gallus gallus
450083 Danio rerio
465761 Pan troglodytes
480988 Canis lupus familiaris
532742 Bos taurus
703129 Macaca mulatta
734749 Xenopus laevis
100022779 Monodelphis domestica
100060370 Equus caballus
100145767 Xenopus (Silurana) tropicalis
100344610 Oryctolagus cuniculus
100409841 Callithrix jacchus
100480888 Ailuropoda melanoleuca
100595113 Nomascus leucogenys
988766 Clostridium perfringens str. 13
1021683 Bifidobacterium longum NCC2705
1028243 Streptococcus mutans UA159
1095964 Streptomyces coelicolor A3(2)
1174420 Yersinia pestis CO92
1255824 Salmonella enterica subsp. enterica serovar Typhimurium str. LT2
2956399 Yersinia pseudotuberculosis IP 32953
3977399 Lactobacillus salivarius UCC118
4983447 Aspergillus niger CBS 513.88
4987403 Aspergillus niger CBS 513.88
5989256 Aspergillus oryzae RIB40
6032795 Culex quinquefasciatus
7264928 Bifidobacterium animalis subsp. lactis AD011
9223595 Arthroderma otae CBS 113480
9226616 Arthroderma otae CBS 113480
9450395 Brachyspira pilosicoli 95/1000
10899858 Trichinella spiralis
10903123 Trichinella spiralis
99412 Mus musculus
100718405 Cavia porcellus
407057 Sus scrofa
Ausgewählte Anbieter für GLA (GLA) ELISA Kits
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