PEX19 Antikörper (C-Term)

Produktnummer ABIN926758

Dieser Kaninchen Polyklonal Antikörper detektiert spezifisch PEX19 in WB. Es zeigt Reaktivität gegenüber Proben von Human.

Kurzübersicht für PEX19 Antikörper (C-Term) (ABIN926758)

Target: PEX19 (Peroxisomal Biogenesis Factor 19 (PEX19))

Reaktivität: Human

Wirt: Kaninchen

Klonalität: Polyklonal

Konjugat: Dieser PEX19 Antikörper ist unkonjugiert

Applikation: Western Blotting (WB)

Produktdetails anti-PEX19 Antikörper

Bindungsspezifität: C-Term

Aufreinigung: Purified

Immunogen: PEX19 antibody was raised in rabbit using the C terminal of PEX19 as the immunogen

Anwendungsinformationen

Applikationshinweise: Optimal conditions should be determined by the investigator.

Kommentare:

PEX19 Blocking Peptide, (ABIN936282), is also available for use as a blocking control in assays to test for specificity of this PEX19 antibody

Beschränkungen: Nur für Forschungszwecke einsetzbar

Handhabung

Format: Lyophilized

Konzentration: Lot specific

Buffer: Lyophilized powder. Add 50 µL of distilled water. Final antibody concentration is 1 mg/mL in PBS buffer.

Handhabung: Avoid repeated freeze/thaw cycles.

Lagerung: 4 °C/-20 °C

Informationen zur Lagerung: Store at 4 °C, following reconstitution, aliquot and store at -20 °C.

Details zu PEX19

Target: PEX19 (Peroxisomal Biogenesis Factor 19 (PEX19))

Andere Bezeichnung: PEX19

Hintergrund: This gene is necessary for early peroxisomal biogenesis. It acts both as a cytosolic chaperone and as an import receptor for peroxisomal membrane proteins (PMPs). Peroxins (PEXs) are proteins that are essential for the assembly of functional peroxisomes. The peroxisome biogenesis disorders (PBDs) are a group of genetically heterogeneous autosomal recessive, lethal diseases characterized by multiple defects in peroxisome function. These disorders have at least 14 complementation groups, with more than one phenotype being observed for some complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene are a cause of Zellweger syndrome (ZWS), as well as peroxisome biogenesis disorder complementation group 14 (PBD-CG14), which is also known as PBD-CGJ. Alternative splicing results in multiple transcript variants. Synonyms: Polyclonal PEX19 antibody, Anti-PEX19 antibody, peroxisomal biogenesis factor 19 antibody, D1S2223E antibody, FLJ55296 antibody, HK33 antibody, PMP1 antibody, PMPI antibody, PXF antibody, PXMP1 antibody.