Der Kaninchen Polyklonal Anti-LRPPRC-Antikörper wurde für IHC und IF validiert. Er ist geeignet, LRPPRC in Proben von Human, Maus und Ratte zu detektieren.
LRPPRC,CLONE-23970,GP130,LRP130,LSFC,This gene encodes a leucine-rich protein that has multiple pentatricopeptide repeats (PPR). The precise role of this protein is unknown but studies suggest it may play a role in cytoskeletal organization, vesicular transport, or in transcriptional regulation of both nuclear and mitochondrial genes. The protein localizes primarily to mitochondria and is predicted to have an N-terminal mitochondrial targeting sequence. Mutations in this gene are associated with the French-Canadian type of Leigh syndrome.