SBDS Antikörper (AA 1-250)
Kurzübersicht für SBDS Antikörper (AA 1-250) (ABIN5775988)
Target
Alle SBDS Antikörper anzeigenReaktivität
Wirt
Klonalität
Konjugat
Applikation
Klon
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Bindungsspezifität
- AA 1-250
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Immunogen
- Recombinant human SBDS (1-250aa) purified from E. coli
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Isotyp
- IgG2b kappa
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Beschränkungen
- Nur für Forschungszwecke einsetzbar
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Format
- Liquid
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Konzentration
- 1 mg/mL
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Lagerung
- 4 °C,-20 °C,-80 °C
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Informationen zur Lagerung
- Can be stored at +2°C to +8°C for 1 week. For long term storage, aliquot and store at -20°C to -80°C. Avoid repeated freezing and thawing cycles.
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- SBDS (Shwachman-Bodian-Diamond Syndrome (SBDS))
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Andere Bezeichnung
- SBDS
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Hintergrund
- The Shwachman-Bodian-Diamond syndrome (SBDS) is 249 amino acid ribosome maturation protein. The precise function of the SBDS protein is not known but it appears to play an important role in actin cytoskeletal function and mitotic spindle stabilization. Also, SBDS is required for the assembly of mature ribosomes and ribosome biogenesis. Mutations in the SBDS gene cause Shwachman-Diamond syndrome (SDS). SDS is an autosomal recessive disorder with clinical features that include pancreatic exocrine insufficiency, haematological dysfunction and skeletal abnormalities.
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NCBI Accession
- NP_057122
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Pathways
- Ribonucleoprotein Complex Subunit Organization, Ribosome Assembly
Target
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