FKRP Antikörper (AA 237-265)

Produktnummer ABIN5536570

Produktdetails anti-FKRP Antikörper

Target: FKRP (Fukutin Related Protein (FKRP))

Bindungsspezifität: AA 237-265

Reaktivität: Human

Wirt: Kaninchen

Klonalität: Polyklonal

Konjugat: Dieser FKRP Antikörper ist unkonjugiert

Applikation: Western Blotting (WB)

Aufreinigung: This antibody is purified through a protein A column, followed by peptide affinity purification.

Immunogen: This FKRP antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide between 237-265 amino acids from the Central region of human FKRP.

Isotyp: Ig Fraction

Anwendungsinformationen

Applikationshinweise: For WB starting dilution is: 1:1000

Beschränkungen: Nur für Forschungszwecke einsetzbar

Handhabung

Format: Liquid

Konzentration: 0.5 mg/mL

Buffer: Supplied in PBS with 0.09 % (W/V) sodium azide.

Konservierungsmittel: Sodium azide

Vorsichtsmaßnahmen: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Lagerung: 4 °C,-20 °C

Informationen zur Lagerung: Store at 4°C for three months and -20°C, stable for up to one year. As with all antibodies care should be taken to avoid repeated freeze thaw cycles. Antibodies should not be exposed to prolonged high temperatures.

Details zu FKRP

Target: FKRP (Fukutin Related Protein (FKRP))

Andere Bezeichnung: FKRP (FKRP Produkte)

Synonyme: zgc:162829 antikoerper, LGMD2I antikoerper, MDC1C antikoerper, MDDGA5 antikoerper, MDDGB5 antikoerper, MDDGC5 antikoerper, A830029B19Rik antikoerper, AI842067 antikoerper, AI847300 antikoerper, LGMD1I antikoerper, fukutin related protein antikoerper, FKRP antikoerper, fkrp antikoerper, Fkrp antikoerper

Hintergrund: This gene encodes a protein which is targeted to the medial Golgi apparatus and is necessary for posttranslational modification of dystroglycan. Mutations in this gene have been associated with congenital muscular dystrophy, mental retardation, and cerebellar cysts. Several alternatively spliced transcript variants of this gene have been described, but the full-length nature of some of these variants has not been determined. [provided by RefSeq].

Molekulargewicht: 55 kDa

Gen-ID: 79147

UniProt: Q9H9S5

Pathways: Regulation of Carbohydrate Metabolic Process