FKRP Antikörper (C-Term)

Produktnummer ABIN1536611

Produktdetails anti-FKRP Antikörper

Target: FKRP (Fukutin Related Protein (FKRP))

Bindungsspezifität: AA 418-444, C-Term

Reaktivität: Human

Wirt: Maus

Klonalität: Monoklonal

Konjugat: Dieser FKRP Antikörper ist unkonjugiert

Applikation: Western Blotting (WB)

Homologie: M

Aufreinigung: This antibody is purified through a protein G column, followed by dialysis against PBS.

Immunogen: This FKRP antibody is generated from mice immunized with a KLH conjugated synthetic peptide between 418-444 amino acids from the C-terminal region of human FKRP.

Klon: 386CT13-1-9

Isotyp: IgG1

Anwendungsinformationen

Applikationshinweise: WB: 1:100

Beschränkungen: Nur für Forschungszwecke einsetzbar

Handhabung

Format: Liquid

Buffer: Purified monoclonal antibody supplied in PBS with 0.09 % (W/V) sodium azide.

Konservierungsmittel: Sodium azide

Vorsichtsmaßnahmen: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Lagerung: 4 °C,-20 °C

Informationen zur Lagerung: FKRP Antibody (C-term) can be refrigerated at 2-8 °C for up to 6 months. For long term storage, keep at -20 °C.

Haltbarkeit: 6 months

Details zu FKRP

Target: FKRP (Fukutin Related Protein (FKRP))

Andere Bezeichnung: FKRP (FKRP Produkte)

Synonyme: zgc:162829 antikoerper, LGMD2I antikoerper, MDC1C antikoerper, MDDGA5 antikoerper, MDDGB5 antikoerper, MDDGC5 antikoerper, A830029B19Rik antikoerper, AI842067 antikoerper, AI847300 antikoerper, LGMD1I antikoerper, fukutin related protein antikoerper, FKRP antikoerper, fkrp antikoerper, Fkrp antikoerper

Hintergrund: This gene encodes a protein which is targeted to the medial Golgi apparatus and is necessary for posttranslational modification of dystroglycan. Mutations in this gene have been associated with congenital muscular dystrophy, mental retardation, and cerebellar cysts. Several alternatively spliced transcript variants of this gene have been described, but the full-length nature of some of these variants has not been determined. [provided by RefSeq].

Molekulargewicht: 54568

Gen-ID: 79147

NCBI Accession: NP_001034974, NP_077277

UniProt: Q9H9S5

Pathways: Regulation of Carbohydrate Metabolic Process