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Dysferlin Antikörper (AA 1901-2119) (AbBy Fluor® 594)

This anti-Dysferlin antibody (ABIN2812578) is a Rabbit Polyclonal antibody detecting Dysferlin in FACS. Suitable for Human.
Produktnummer ABIN2812578

Kurzübersicht für Dysferlin Antikörper (AA 1901-2119) (AbBy Fluor® 594) (ABIN2812578)

Target

Alle Dysferlin (DYSF) Antikörper anzeigen
Dysferlin (DYSF)

Reaktivität

  • 59
  • 25
  • 5
  • 4
  • 4
  • 4
  • 4
  • 2
  • 2
  • 2
  • 2
Human

Wirt

  • 53
  • 5
  • 1
Kaninchen

Klonalität

  • 46
  • 13
Polyklonal

Konjugat

  • 27
  • 4
  • 3
  • 2
  • 2
  • 2
  • 2
  • 2
  • 2
  • 2
  • 1
  • 1
  • 1
  • 1
  • 1
  • 1
  • 1
  • 1
  • 1
  • 1
  • 1
Dieser Dysferlin Antikörper ist konjugiert mit AbBy Fluor® 594

Applikation

  • 20
  • 17
  • 15
  • 14
  • 9
  • 7
  • 5
  • 2
  • 2
  • 1
  • 1
Flow Cytometry (FACS)
  • Bindungsspezifität

    • 15
    • 6
    • 6
    • 2
    • 2
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    AA 1901-2119

    Kreuzreaktivität

    Human

    Homologie

    Mouse,Rat,Dog,Cow,Pig,Horse,Rabbit,Guinea Pig

    Aufreinigung

    Purified by Protein A.

    Immunogen

    KLH conjugated synthetic peptide derived from human DYSF

    Isotyp

    IgG
  • Applikationshinweise

    FCM 1:20-100

    Beschränkungen

    Nur für Forschungszwecke einsetzbar
  • Format

    Liquid

    Konzentration

    1 μg/μL

    Buffer

    Aqueous buffered solution containing 0.01M TBS ( pH 7.4) with 1 % BSA, 0.03 % Proclin300 and 50 % Glycerol.

    Konservierungsmittel

    ProClin

    Vorsichtsmaßnahmen

    This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE, which should be handled by trained staff only.

    Lagerung

    -20 °C

    Informationen zur Lagerung

    Store at -20°C. Aliquot into multiple vials to avoid repeated freeze-thaw cycles.

    Haltbarkeit

    12 months
  • Target

    Dysferlin (DYSF)

    Andere Bezeichnung

    Dysferlin

    Hintergrund

    Synonyms: DMAT, DYSF, Dysferlin Dystrophy associated fer 1 like protein Fer 1 like protein 1, Dysferlin limb girdle muscular dystrophy 2B autosomal recessive, Dysferlin limb girdle muscular dystrophy 2B, Dystrophy associated fer 1 like 1, Dystrophy associated fer 1 like protein, Dystrophy associated fer1 like 1, Dystrophy associated fer1 like protein, Fer 1 like protein 1, Fer1 like protein 1, FER1L1, FLJ00175, FLJ90168, LGMD 2B, LGMD2B, Limb girdle muscular dystrophy 2B autosomal recessive , Limb girdle muscular dystrophy 2B, Miyoshi myopathy, MM, DYSF_HUMAN.

    Background: The protein encoded by this gene belongs to the ferlin family and is a skeletal muscle protein found associated with the sarcolemma. It is involved in muscle contraction and contains C2 domains that play a role in calcium-mediated membrane fusion events, suggesting that it may be involved in membrane regeneration and repair. In addition, the protein encoded by this gene binds caveolin-3, a skeletal muscle membrane protein which is important in the formation of caveolae. Specific mutations in this gene have been shown to cause autosomal recessive limb girdle muscular dystrophy type 2B (LGMD2B) as well as Miyoshi myopathy. Alternative splicing results in multiple transcript variants. [provided by RefSeq, Aug 2008].

    Gen-ID

    8291

    UniProt

    O75923
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