CLN6 Antikörper
Kurzübersicht für CLN6 Antikörper (ABIN2459097)
Target
Alle CLN6 Antikörper anzeigenReaktivität
Wirt
Klonalität
Konjugat
Applikation
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Aufreinigung
- Antibody is purified by peptide affinity chromatography method.
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Immunogen
- Antibody produced in rabbits immunized with a synthetic peptide corresponding a region of human CLN6.
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anti-Ceroid-Lipofuscinosis, Neuronal 6, Late Infantile, Variant (CLN6) (Internal Region) antibody
CLN6 Reaktivität: Human, Maus, Ratte WB, ELISA, IHC, IF, ICC Wirt: Kaninchen Polyclonal unconjugated
anti-Ceroid-Lipofuscinosis, Neuronal 6, Late Infantile, Variant (CLN6) (AA 1-43) antibodyCLN6 Reaktivität: Human ELISA, IHC Wirt: Kaninchen Polyclonal unconjugated
anti-Ceroid-Lipofuscinosis, Neuronal 6, Late Infantile, Variant (CLN6) (AA 108-157) antibodyCLN6 Reaktivität: Human, Maus, Ratte, Hund, Pferd, Meerschweinchen, Fledermaus, Affe, Huhn WB Wirt: Kaninchen Polyclonal unconjugated
anti-Ceroid-Lipofuscinosis, Neuronal 6, Late Infantile, Variant (CLN6) (C-Term) antibodyCLN6 Reaktivität: Human, Maus, Ratte, Hund, Pferd, Rind (Kuh), Kaninchen, Schaf, Zebrafisch (Danio rerio), Schwein, Fledermaus, Affe WB Wirt: Kaninchen Polyclonal unconjugated
anti-Ceroid-Lipofuscinosis, Neuronal 6, Late Infantile, Variant (CLN6) (C-Term) antibodyCLN6 Reaktivität: Human, Maus, Ratte, Hund WB Wirt: Kaninchen Polyclonal unconjugated
anti-Ceroid-Lipofuscinosis, Neuronal 6, Late Infantile, Variant (CLN6) (AA 221-270) antibodyCLN6 Reaktivität: Human WB, ELISA, IHC Wirt: Kaninchen Polyclonal unconjugated
anti-Ceroid-Lipofuscinosis, Neuronal 6, Late Infantile, Variant (CLN6) (C-Term) antibodyCLN6 Reaktivität: Human, Maus, Ratte, Hund, Pferd, Meerschweinchen, Rind (Kuh), Kaninchen, Schaf, Zebrafisch (Danio rerio), Schwein WB, IHC Wirt: Kaninchen Polyclonal unconjugated
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Applikationshinweise
- CLN6 antibody can be used for detection of CLN6 by ELISA at 1:1562500. CLN6 antibody can be used for detection of CLN6 by western blot at 1 μg/mL, and HRP conjugated secondary antibody should be diluted 1:50,000 - 100,000.
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Beschränkungen
- Nur für Forschungszwecke einsetzbar
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Format
- Lyophilized
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Rekonstitution
- Add 50 ?L of distilled water. Final antibody concentration is 1 mg/mL.
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Konzentration
- 1 mg/mL
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Buffer
- Antibody is lyophilized in PBS buffer with 2 % sucrose.
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Handhabung
- As with any antibody avoid repeat freeze-thaw cycles.
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Lagerung
- 4 °C/-20 °C
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Informationen zur Lagerung
- For short periods of storage (days) store at 4 °C. For longer periods of storage, store CLN6 antibody at -20 °C.
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- CLN6 (Ceroid-Lipofuscinosis, Neuronal 6, Late Infantile, Variant (CLN6))
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Andere Bezeichnung
- CLN6
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Hintergrund
- CLN6 is one of eight which have been associated with neuronal ceroid lipofuscinoses (NCL). Also referred to as Batten disease, NCL comprises a class of autosomal recessive, neurodegenerative disorders affecting children. The genes responsible likely CLN6 involved in the degradation of post-translationally modified proteins in lysosomes. The primary defect in NCL disorders is thought to be associated with lysosomal storage function.
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Molekulargewicht
- 36 kDa
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Gen-ID
- 54982
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NCBI Accession
- NP_060352
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UniProt
- Q9NWW5
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Pathways
- Glycosaminoglycan Metabolic Process
Target
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