PEX19 Antikörper (AA 1-269)
Kurzübersicht für PEX19 Antikörper (AA 1-269) (ABIN1885873)
Target
Alle PEX19 Antikörper anzeigenReaktivität
Wirt
Klonalität
Konjugat
Applikation
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Bindungsspezifität
- AA 1-269
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Aufreinigung
- Purified by antigen-affinity chromatography.
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Immunogen
- Recombinant protein fragment contain a sequence corresponding to a region within amino acids 1 and 269 of PEX19
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Applikationshinweise
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Suggested dilutions:
Western blotting: 1.500-1.3000
Immunohistochemistry: 1.100-1.500
Immunofluorescence: 1.100-1.200 -
Beschränkungen
- Nur für Forschungszwecke einsetzbar
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Format
- Liquid
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Buffer
- 0.1 M Tris-buffered saline with 10 % Glycerol (pH 7.0).0.01 % Thimerosal was added as a preservative.
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Konservierungsmittel
- Thimerosal (Merthiolate)
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Vorsichtsmaßnahmen
- Biohazard Informations: This product contains thimerosal which is hazardous.
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Lagerung
- 4 °C/-20 °C
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Informationen zur Lagerung
- Store at -20 °C for long term preservation (recommended). Store at 4 °C for short term use.
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- PEX19 (Peroxisomal Biogenesis Factor 19 (PEX19))
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Andere Bezeichnung
- PEX19
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Hintergrund
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This gene is necessary for early peroxisomal biogenesis.It acts both as a cytosolic chaperone and as an import receptor for peroxisomal membrane proteins (PMPs).Peroxins (PEXs) are proteins that are essential for the assembly of functional peroxisomes.The peroxisome biogenesis disorders (PBDs) are a group of genetically heterogeneous autosomal recessive, lethal diseases characterized by multiple defects in peroxisome function.The peroxisomal biogenesis disorders are a heterogeneous group with at least 14 complementation groups and with more than 1 phenotype being observed in cases falling into particular complementation groups.Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle.Defects in this gene are a cause Zellweger syndrome (ZWS).[provided by RefSeq]
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Molekulargewicht
- 33 kDa
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Gen-ID
- 5824
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NCBI Accession
- NP_002848, NM_002857
Target
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