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ALDH6A1 Produkte

(Aldehyde Dehydrogenase 6 Family, Member A1 (ALDH6A1))

Kategorien

This protein belongs to the aldehyde dehydrogenases family of proteins. This enzyme plays a role in the valine and pyrimidine catabolic pathways. The product of this gene, a mitochondrial methylmalonate semialdehyde dehydrogenase, catalyzes the irreversible oxidative decarboxylation of malonate and methylmalonate semialdehydes to acetyl- and propionyl-CoA. Methylmalonate semialdehyde dehydrogenase deficiency is characterized by elevated beta-alanine, 3-hydroxypropionic acid, and both isomers of 3-amino and 3-hydroxyisobutyric acids in urine organic acids. [provided by RefSeq, Jul 2008].

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Ausgewählte ALDH6A1 Kategorien

ALDH6A1 Antikörper

High quality antibodies with extensive validation data.

ALDH6A1 ELISA Kits

Reliable ELISA kits for a wide range of species.

ALDH6A1 Proteine

Proteins for various applications incl. WB, ELISA, IF etc.

Empfohlene ALDH6A1 Antikörper

Produkt
Reaktivität
Applikation
Validierungen
Kat. Nr.
Menge
Datenblatt
Reaktivität Human
Applikation WB, ELISA, IHC, FACS, ICC
Validierungen
  • (9)
Kat. Nr. ABIN5542265
Menge 0.1 mg
Datenblatt Datenblatt
Reaktivität Human
Applikation WB, IHC (p), IF
Validierungen
  • (4)
Kat. Nr. ABIN659006
Menge 400 μL
Datenblatt Datenblatt
Reaktivität Human
Applikation WB, IHC (p)
Validierungen
  • (4)
Kat. Nr. ABIN2855626
Menge 100 μL
Datenblatt Datenblatt

Empfohlene ALDH6A1 ELISA Kits

Produkt
Reaktivität
Analytical Method
Validierungen
Kat. Nr.
Menge
Datenblatt
Reaktivität Human
Analytical Method Quantitative Sandwich ELISA
Validierungen
  • (1)
Kat. Nr. ABIN6953596
Menge 96 tests
Datenblatt Datenblatt
Reaktivität Mouse
Analytical Method
Validierungen
Kat. Nr. ABIN1142386
Menge 96 tests
Datenblatt Datenblatt
Reaktivität Rat
Analytical Method
Validierungen
Kat. Nr. ABIN1142387
Menge 96 tests
Datenblatt Datenblatt

Empfohlene ALDH6A1 Proteine

Produkt
Reaktivität
Source
Validierungen
Kat. Nr.
Menge
Datenblatt
Reaktivität Human
Source Wheat germ
Validierungen
  • (1)
Kat. Nr. ABIN1344841
Menge 10 μg
Datenblatt Datenblatt
Reaktivität Human
Source Escherichia coli (E. coli)
Validierungen
  • (1)
Kat. Nr. ABIN7121777
Menge 50 μg
Datenblatt Datenblatt
Reaktivität Human
Source Insect Cells
Validierungen
  • (1)
Kat. Nr. ABIN3083766
Menge 1 mg
Datenblatt Datenblatt

Neueste Publikationen zu unseren ALDH6A1 Produkten

Jeon, Jeong, Baek, Koo, Park, Yang, Yu, Kim, Pak: "Network clustering revealed the systemic alterations of mitochondrial protein expression." in: PLoS computational biology, Vol. 7, Issue 6, pp. e1002093, (2011) (PubMed).

Alnouti, Klaassen: "Tissue distribution, ontogeny, and regulation of aldehyde dehydrogenase (Aldh) enzymes mRNA by prototypical microsomal enzyme inducers in mice." in: Toxicological sciences : an official journal of the Society of Toxicology, Vol. 101, Issue 1, pp. 51-64, (2007) (PubMed).

Kuiper, Williams, Distl, Drögemüller: "Assignment of the PAX6 gene to bovine chromosome 15q25-->q27 by fluorescence in situ hybridization and confirmation by radiation hybrid mapping." in: Cytogenetic and genome research, Vol. 109, Issue 4, pp. 533, (2005) (PubMed).

Anderson, Polanski, Pieper, Gatlin, Tirumalai, Conrads, Veenstra, Adkins, Pounds, Fagan, Lobley: "The human plasma proteome: a nonredundant list developed by combination of four separate sources." in: Molecular & cellular proteomics : MCP, Vol. 3, Issue 4, pp. 311-26, (2004) (PubMed).

Chambliss, Gray, Rylance, Pollitt, Gibson: "Molecular characterization of methylmalonate semialdehyde dehydrogenase deficiency." in: Journal of inherited metabolic disease, Vol. 23, Issue 5, pp. 497-504, (2000) (PubMed).

Synonyme und alternative Namen zu ALDH6A1

aldehyde dehydrogenase 6 family member A1 (ALDH6A1), aldehyde dehydrogenase 6 family, member A1 (Aldh6a1), aldehyde dehydrogenase 6 family member A1 L homeolog (aldh6a1.L), methylmalonic acid semialdehyde dehydrogenase (CCNA_02357), aldehyde dehydrogenase 6 family, member A1 (aldh6a1), methylmalonate-semialdehyde dehydrogenase (CoA acylating) (VAA_RS07845), aldehyde dehydrogenase family 6, subfamily A1 (Aldh6a1), aldehyde dehydrogenase 6 family member A1 (Aldh6a1), 1110038I05Rik, AI314632, cb850, MMSADHA, MMSDH, Mmsdh, wu:fb03a04, zgc:92082

Bezeichner auf Proteinebene für ALDH6A1

  • malonate-semialdehyde dehydrogenase
  • methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial
  • mitochondrial acylating methylmalonate-semialdehyde dehydrogenase
  • aldehyde dehydrogenase family 6 member A1
  • aldehyde dehydrogenase family 6, subfamily A1
  • methylmalonate semialdehyde dehydrogenase
  • MMSDH
  • aldehyde dehydrogenase 6A1
  • aldehyde dehydrogenase 6 family, member A1
  • methylmalonate-semialdehyde dehydrogenase [acylating], mitochondrial-like
  • Malonate-semialdehyde dehydrogenase
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