A synthetic peptide for use as a blocking control in assays to test for specificity of GAA antibody, Alternative Names: GAA control peptide, GAA antibody Blocking Peptide, Anti-GAA Blocking Peptide, Glucosidase Alpha, Acid Blocking Peptide, LYAG Blocking Peptide
GAA
Reaktivität: Human
Wirt: Synthetic
BP, IHC, WB
Applikationshinweise
Optimal conditions should be determined by the investigator
Beschränkungen
Nur für Forschungszwecke einsetzbar
Format
Lyophilized
Rekonstitution
Add 100 µL of distilled water for a final peptide concentration is 1 mg/mL.
Buffer
PBS
Handhabung
Avoid repeated freeze/thaw cycles.
Lagerung
-20 °C
Informationen zur Lagerung
Store at -20 °C long term.
Target
GAA
(Glucosidase, Alpha, Acid (GAA))
Hintergrund
GAA is acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes. Different forms of acid alpha-glucosidase are obtained by proteolytic processing. Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum.