Propionyl CoA Carboxylase beta Polypeptide Proteine (PCCB)

The protein encoded by this gene is a subunit of the propionyl-CoA carboxylase (PCC) enzyme, which is involved in the catabolism of propionyl-CoA. PCC is a mitochondrial enzyme that probably acts as a dodecamer of six alpha subunits and six beta subunits. This gene encodes the beta subunit of PCC. Defects in this gene are a cause of propionic acidemia type II (PA-2). Multiple transcript variants encoding different isoforms have been found for this gene.

• propionyl-CoA carboxylase beta subunit (PCCB)
• propionyl-CoA carboxylase beta subunit (Pccb)
• propionyl Coenzyme A carboxylase, beta polypeptide (Pccb)

• 1300012P06Rik Protein
• AI314687 Protein
• R74805 Protein

PCCase subunit beta , propanoyl-CoA:carbon dioxide ligase subunit beta , propionyl Coenzyme A carboxylase, beta polypeptide , propionyl-CoA carboxylase beta chain, mitochondrial , propionyl coenzyme A carboxylase, beta polypeptide , PCCase beta subunit , propanoyl-CoA:carbon dioxide ligase beta subunit