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DBT Produkte

(Dihydrolipoamide Branched Chain Transacylase E2 (DBT))

Kategorien

The branched-chain alpha-keto acid dehydrogenase complex (BCKD) is an inner-mitochondrial enzyme complex involved in the breakdown of the branched-chain amino acids isoleucine, leucine, and valine. The BCKD complex is thought to be composed of a core of 24 transacylase (E2) subunits, and associated decarboxylase (E1), dehydrogenase (E3), and regulatory subunits. This gene encodes the transacylase (E2) subunit. Mutations in this gene result in maple syrup urine disease, type 2. Alternatively spliced transcript variants have been described, but their biological validity has not been determined. [provided by RefSeq, Jul 2008].

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Ausgewählte DBT Kategorien

DBT Antikörper

High quality antibodies with extensive validation data.

DBT ELISA Kits

Reliable ELISA kits for a wide range of species.

DBT Proteine

Proteins for various applications incl. WB, ELISA, IF etc.

Empfohlene DBT Antikörper

Produkt
Reaktivität
Applikation
Validierungen
Kat. Nr.
Menge
Datenblatt
Reaktivität Human
Applikation WB
Validierungen
  • (1)
  • (3)
Kat. Nr. ABIN514887
Menge 50 μg
Datenblatt Datenblatt
Reaktivität Bat, Cow, Dog, Guinea Pig, Horse, Human, Monkey, Mouse, Pig, Rabbit, Rat
Applikation WB, IHC, IHC (p)
Validierungen
  • (4)
Kat. Nr. ABIN6745750
Menge 100 μL
Datenblatt Datenblatt
Reaktivität Human
Applikation WB
Validierungen
  • (3)
Kat. Nr. ABIN947782
Menge 100 μg
Datenblatt Datenblatt

Empfohlene DBT ELISA Kits

Produkt
Reaktivität
Analytical Method
Validierungen
Kat. Nr.
Menge
Datenblatt
Reaktivität Human
Analytical Method Quantitative Sandwich ELISA
Validierungen
  • (1)
Kat. Nr. ABIN6966364
Menge 96 tests
Datenblatt Datenblatt
Reaktivität Human
Analytical Method
Validierungen
Kat. Nr. ABIN1140790
Menge 96 tests
Datenblatt Datenblatt
Reaktivität Cow
Analytical Method
Validierungen
Kat. Nr. ABIN1140789
Menge 96 tests
Datenblatt Datenblatt

Empfohlene DBT Proteine

Produkt
Reaktivität
Source
Validierungen
Kat. Nr.
Menge
Datenblatt
Reaktivität Human
Source Escherichia coli (E. coli)
Validierungen
  • (1)
Kat. Nr. ABIN3084921
Menge 1 mg
Datenblatt Datenblatt
Reaktivität Mouse
Source Escherichia coli (E. coli)
Validierungen
  • (1)
Kat. Nr. ABIN3134462
Menge 1 mg
Datenblatt Datenblatt
Reaktivität Human
Source HEK-293 Cells
Validierungen
  • (1)
Kat. Nr. ABIN2719240
Menge 20 μg
Datenblatt Datenblatt

Neueste Publikationen zu unseren DBT Produkten

Johnson, Vidoni, Durigon, Pearce, Rorbach, He, Brea-Calvo, Minczuk, Reyes, Holt, Spinazzola: "Amino acid starvation has opposite effects on mitochondrial and cytosolic protein synthesis." in: PLoS ONE, Vol. 9, Issue 4, pp. e93597, (2014) (PubMed).

Fredersdorf, Milne, Hall, Lu: "Characterization of a panel of novel anti-p21Waf1/Cip1 monoclonal antibodies and immunochemical analysis of p21Waf1/Cip1 expression in normal human tissues." in: The American journal of pathology, Vol. 148, Issue 3, pp. 825-35, (1997) (PubMed).

Levine: "p53, the cellular gatekeeper for growth and division." in: Cell, Vol. 88, Issue 3, pp. 323-31, (1997) (PubMed).

Synonyme und alternative Namen zu DBT

dihydrolipoamide branched chain transacylase E2 (DBT), dihydrolipoamide branched chain transacylase E2 (dbt), dihydrolipoamide branched chain transacylase E2 (CpipJ_CPIJ006326), dihydrolipoamide branched chain transacylase E2 (BDBG_05874), dihydrolipoamide branched chain transacylase E2 (NAEGRDRAFT_78509), dihydrolipoamide branched chain transacylase E2 (VDBG_04820), hypothetical protein (PGTG_17722), dihydrolipoamide branched chain transacylase E2 (Dbt), dihydrolipoamide branched chain transacylase E2 L homeolog (dbt.L), BCATE2, BCKAD-E2, BCKADE2, D3Wsu60e, E2, E2B, E2b, im:7147214, zgc:103768

Bezeichner auf Proteinebene für DBT

  • lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrial
  • dihydrolipoamide branched chain transacylase E2
  • BCKAD E2 subunit
  • E2 component of branched chain alpha-keto acid dehydrogenase complex
  • branched chain acyltransferase, E2 component
  • branched-chain alpha-keto acid dehydrogenase complex component E2
  • dihydrolipoamide acetyltransferase component of branched-chain alpha-keto acid dehydrogenase complex
  • dihydrolipoyl transacylase
  • dihydrolipoyllysine-residue (2-methylpropanoyl)transferase
  • lipoamide acyltransferase component of mitochondrial branched-chain alpha-keto acid dehydrogenase complex
  • mitochondrial branched chain alpha-keto acid dehydrogenase transacylase subunit (E2b)
  • BCKAD E2
  • BCKAD-E2
  • BCKADE2
  • branched-chain alpha-ketoacid dehydrogenase, E2 subunit
  • part of the BCKAD complex
  • que
  • mitochondrial branched-chain alpha-keto acid dihydrolipoyl acyltransferase
  • component of branched chain keto acid dehydrogenase complex
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