GNS Antikörper (C-Term)

Produktnummer ABIN928079

Der Kaninchen Polyklonal Anti-GNS-Antikörper wurde für WB validiert. Er ist geeignet, GNS in Proben von Human und Ratte zu detektieren.

Kurzübersicht für GNS Antikörper (C-Term) (ABIN928079)

Target: GNS (Glucosamine (N-Acetyl)-6-Sulfatase (GNS))

Reaktivität: Human, Ratte

Wirt: Kaninchen

Klonalität: Polyklonal

Konjugat: Dieser GNS Antikörper ist unkonjugiert

Applikation: Western Blotting (WB)

Produktdetails anti-GNS Antikörper

Bindungsspezifität: C-Term

Kreuzreaktivität: Ratte (Rattus)

Aufreinigung: Purified

Immunogen: Gns antibody was raised in rabbit using the C terminal of Gns as the immunogen

Anwendungsinformationen

Applikationshinweise: WB: 0.2-1 µg/mL
Optimal conditions should be determined by the investigator.

Kommentare:

Gns Blocking Peptide, (ABIN936100), is also available for use as a blocking control in assays to test for specificity of this Gns antibody

Beschränkungen: Nur für Forschungszwecke einsetzbar

Handhabung

Format: Lyophilized

Konzentration: Lot specific

Buffer: Lyophilized powder. Add 50 µL of distilled water. Final antibody concentration is 1 mg/mL in PBS buffer.

Handhabung: Avoid repeated freeze/thaw cycles.

Lagerung: 4 °C/-20 °C

Informationen zur Lagerung: Store at 4 °C, following reconstitution, aliquot and store at -20 °C.

Details zu GNS

Target: GNS (Glucosamine (N-Acetyl)-6-Sulfatase (GNS))

Andere Bezeichnung: Gns

Hintergrund: GNS is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparin sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder ucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome. Synonyms: Polyclonal Gns antibody, Anti-Gns antibody, glucosamine, N-acetyl-6-sulfatase antibody, Gns antibody.

Pathways: Glycosaminoglycan Metabolic Process