ALAD Antikörper (AA 151-240) (FITC)

Produktnummer ABIN882123

Produktdetails anti-ALAD Antikörper (FITC)

Target: ALAD (Aminolevulinate Dehydratase (ALAD))

Bindungsspezifität: AA 151-240

Reaktivität: Maus

Wirt: Kaninchen

Klonalität: Polyklonal

Konjugat: Dieser ALAD Antikörper ist konjugiert mit FITC

Applikation: Western Blotting (WB), Immunofluorescence (Cultured Cells) (IF (cc)), Immunofluorescence (Paraffin-embedded Sections) (IF (p))

Kreuzreaktivität: Maus

Homologie: Human,Rat,Dog,Cow,Sheep,Horse,Rabbit

Aufreinigung: Purified by Protein A.

Immunogen: KLH conjugated synthetic peptide derived from human ALAD

Isotyp: IgG

Anwendungsinformationen

Applikationshinweise: IF(IHC-P) 1:50-200
IF(IHC-F) 1:50-200
IF(ICC) 1:50-200

Beschränkungen: Nur für Forschungszwecke einsetzbar

Handhabung

Format: Liquid

Konzentration: 1 μg/μL

Buffer: Aqueous buffered solution containing 0.01M TBS ( pH 7.4) with 1 % BSA, 0.03 % Proclin300 and 50 % Glycerol.

Konservierungsmittel: ProClin

Vorsichtsmaßnahmen: This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE, which should be handled by trained staff only.

Lagerung: -20 °C

Informationen zur Lagerung: Store at -20°C. Aliquot into multiple vials to avoid repeated freeze-thaw cycles.

Haltbarkeit: 12 months

Details zu ALAD

Target: ALAD (Aminolevulinate Dehydratase (ALAD))

Andere Bezeichnung: ALAD (ALAD Produkte)

Synonyme: DDBDRAFT_0190269 antikoerper, DDBDRAFT_0231415 antikoerper, DDB_0190269 antikoerper, DDB_0231415 antikoerper, ALAD antikoerper, ncf antikoerper, ALADH antikoerper, PBGS antikoerper, ALADR antikoerper, aminolevulinatedelta-dehydratase antikoerper, zgc:110219 antikoerper, Lv antikoerper, delta-aminolevulinate dehydratase antikoerper, aminolevulinate dehydratase antikoerper, delta-aminolevulinic acid dehydratase antikoerper, Delta-aminolevulinic acid dehydratase antikoerper, aminolevulinate dehydratase L homeolog antikoerper, aminolevulinate, delta-, dehydratase antikoerper, hemB antikoerper, ALAD antikoerper, PBGS antikoerper, STY0404 antikoerper, SAS1597 antikoerper, SACI_RS03725 antikoerper, PAAG_00299 antikoerper, VDBG_00315 antikoerper, HPPC_00830 antikoerper, MGYG_01952 antikoerper, hem2 antikoerper, alad.L antikoerper, Alad antikoerper, alad antikoerper

Hintergrund:

Synonyms: ALAD, ALADH, ALADR, Aminolevulinate dehydratase, Aminolevulinate, delta, dehydratase, Delta aminolevulinic acid dehydratase, Delta-aminolevulinic acid dehydratase, HEM2_HUMAN, Lv, PBGS, Porphobilinogen synthase.

Background: Catalyzes an early step in the biosynthesis of tetrapyrroles. Binds two molecules of 5-aminolevulinate per subunit, each at a distinct site, and catalyzes their condensation to form porphobilinogen.Involvement in disease:Defects in ALAD are the cause of acute hepatic porphyria (AHP). AHP is a form of porphyria. Porphyrias are inherited defects in the biosynthesis of heme, resulting in the accumulation and increased excretion of porphyrins or porphyrin precursors. They are classified as erythropoietic or hepatic, depending on whether the enzyme deficiency occurs in red blood cells or in the liver. AHP is characterized by attacks of gastrointestinal disturbances, abdominal colic, paralysis, and peripheral neuropathy. Most attacks are precipitated by drugs, alcohol, caloric deprivation, infections, or endocrine factors.

Gen-ID: 210

UniProt: P13716