SGSH Antikörper (AA 206-502)
Kurzübersicht für SGSH Antikörper (AA 206-502) (ABIN8013238)
Target
Alle SGSH Antikörper anzeigenReaktivität
Wirt
Klonalität
Konjugat
Applikation
Güteklasse
-
-
Bindungsspezifität
- AA 206-502
-
Verwendungszweck
- Anti-HSS/SGSH Antibody
-
Kreuzreaktivität (Details)
- No cross-reactivity with other proteins.
-
Produktmerkmale
- Anti-HSS/SGSH Antibody. Tested in ELISA, Flow Cytometry, IHC, WB applications. This antibody reacts with Human, Mouse, Rat.
-
Aufreinigung
- Immunogen affinity purified.
-
Immunogen
- E.coli-derived human HSS/SGSH recombinant protein (Position: R206-L502).
-
Isotyp
- IgG
-
-
-
-
Applikationshinweise
- Western blot, 0.25-0.5 μg/mL, Human, Mouse, Rat Immunohistochemistry(Paraffin-embedded Section), 2-5 μg/mL, Human Flow Cytometry (Fixed), 1-3 μg/1x106 cells, Human ELISA, 0.1-0.5 μg/mL, -
-
Beschränkungen
- Nur für Forschungszwecke einsetzbar
-
-
-
Format
- Lyophilized
-
Rekonstitution
- Adding 0.2 mL of distilled water will yield a concentration of 500 μg/mL.
-
Konzentration
- 500 μg/mL
-
Buffer
- Each vial contains 4 mg Trehalose, 0.9 mg NaCl, 0.2 mg Na2HPO4.
-
Lagerung
- 4 °C,-20 °C
-
Informationen zur Lagerung
-
At -20°C for one year from date of receipt. After reconstitution, at 4°C for one month.
It can also be aliquotted and stored frozen at -20°C for six months. Avoid repeated freezing and thawing. -
Haltbarkeit
- 12 months
-
-
- SGSH (N-Sulfoglucosamine Sulfohydrolase (SGSH))
-
Andere Bezeichnung
- SGSH
-
Hintergrund
-
Background: N-sulphoglucosamine sulphohydrolase is an enzyme that in humans is encoded by the SGSH gene. This gene encodes the enzyme sulfamidase, one of several enzymes involved in the lysosomal degradation of heparan sulfate. Mutations in this gene are associated with the lysosomal storage disease mucopolysaccaridosis IIIA, also known as Sanfilippo syndrome A, which results from impaired degradation of heparan sulfate. Transcripts of varying sizes have been reported but their biological validity has not been determined.
Gene Full Name: N-sulfoglucosamine sulfohydrolase
-
Molekulargewicht
- 57 kDa
-
Gen-ID
- 6448
-
UniProt
- P51688
-
Pathways
- Glycosaminoglycan Metabolic Process
Target
-