D2HGDH Antikörper (AA 322-521)

Produktnummer ABIN7266669

Produktdetails anti-D2HGDH Antikörper

Target: D2HGDH (D-2-Hydroxyglutarate Dehydrogenase (D2HGDH))

Bindungsspezifität: AA 322-521

Reaktivität: Human

Wirt: Kaninchen

Klonalität: Polyklonal

Konjugat: Dieser D2HGDH Antikörper ist unkonjugiert

Applikation: Western Blotting (WB)

Verwendungszweck: D2HGDH Rabbit pAb

Sequenz: GRHLHLASPV QESPFYVLIE TSGSNAGHDA EKLGHFLEHA LGSGLVTDGT MATDQRKVKM LWALRERITE ALSRDGYVYK YDLSLPVERL YDIVTDLRAR LGPHAKHVVG YGHLGDGNLH LNVTAEAFSP SLLAALEPHV YEWTAGQQGS VSAEHGVGFR KRDVLGYSKP PGALQLMQQL KALLDPKGIL NPYKTLPSQA

Kreuzreaktivität: Maus, Ratte

Produktmerkmale: Polyclonal Antibodies

Aufreinigung: Affinity purification

Immunogen: Recombinant fusion protein containing a sequence corresponding to amino acids 322-521 of human D2HGDH (NP_689996.4).

Isotyp: IgG

Anwendungsinformationen

Applikationshinweise: WB,1:500 - 1:2000

Beschränkungen: Nur für Forschungszwecke einsetzbar

Handhabung

Format: Liquid

Buffer: PBS with 0.02 % sodium azide,50 % glycerol, pH 7.3.

Konservierungsmittel: Sodium azide

Vorsichtsmaßnahmen: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Lagerung: -20 °C

Informationen zur Lagerung: Store at -20°C. Avoid freeze / thaw cycles.

Details zu D2HGDH

Target: D2HGDH (D-2-Hydroxyglutarate Dehydrogenase (D2HGDH))

Andere Bezeichnung: D2HGDH (D2HGDH Produkte)

Synonyme: AA408776 antikoerper, AA408778 antikoerper, AI325464 antikoerper, RGD1307976 antikoerper, D2HGD antikoerper, zgc:158661 antikoerper, D-2-hydroxyglutarate dehydrogenase antikoerper, D2hgdh antikoerper, D2HGDH antikoerper, d2hgdh antikoerper

Hintergrund: This gene encodes D-2hydroxyglutarate dehydrogenase, a mitochondrial enzyme belonging to the FAD-binding oxidoreductase/transferase type 4 family. This enzyme, which is most active in liver and kidney but also active in heart and brain, converts D-2-hydroxyglutarate to 2-ketoglutarate. Mutations in this gene are present in D-2-hydroxyglutaric aciduria, a rare recessive neurometabolic disorder causing developmental delay, epilepsy, hypotonia, and dysmorphic features.,D2HGDH,D2HGD,Signal Transduction,Endocrine & Metabolism,D2HGDH

Molekulargewicht: 32kDa/34kDa/56kDa

Gen-ID: 728294

UniProt: Q8N465