CLN8 Antikörper
Kurzübersicht für CLN8 Antikörper (ABIN7266285)
Target
Alle CLN8 Antikörper anzeigenReaktivität
Wirt
Klonalität
Konjugat
Applikation
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Verwendungszweck
- CLN8 Rabbit pAb
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Kreuzreaktivität
- Human
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Produktmerkmale
- Polyclonal Antibodies
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Aufreinigung
- Affinity purification
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Immunogen
- A synthetic peptide of human CLN8.
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Isotyp
- IgG
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anti-Ceroid-Lipofuscinosis, Neuronal 8 (Epilepsy, Progressive with Mental Retardation) (CLN8) (AA 201-286) antibody
CLN8 Reaktivität: Human, Ratte WB, ELISA, IF (cc), IF (p), IHC (fro), IHC (p), ICC Wirt: Kaninchen Polyclonal unconjugated
anti-Ceroid-Lipofuscinosis, Neuronal 8 (Epilepsy, Progressive with Mental Retardation) (CLN8) (AA 251-280), (C-Term) antibodyCLN8 Reaktivität: Human WB Wirt: Kaninchen Polyclonal RB35588 unconjugated
anti-Ceroid-Lipofuscinosis, Neuronal 8 (Epilepsy, Progressive with Mental Retardation) (CLN8) (AA 247-286) antibodyCLN8 Reaktivität: Human ELISA, IHC Wirt: Kaninchen Polyclonal unconjugated
anti-Ceroid-Lipofuscinosis, Neuronal 8 (Epilepsy, Progressive with Mental Retardation) (CLN8) (N-Term) antibodyCLN8 Reaktivität: Human, Hund, Pferd, Affe WB Wirt: Kaninchen Polyclonal unconjugated
anti-Ceroid-Lipofuscinosis, Neuronal 8 (Epilepsy, Progressive with Mental Retardation) (CLN8) (AA 72-121) antibodyCLN8 Reaktivität: Human, Hund, Maus, Rind (Kuh) WB Wirt: Kaninchen Polyclonal unconjugated
anti-Ceroid-Lipofuscinosis, Neuronal 8 (Epilepsy, Progressive with Mental Retardation) (CLN8) antibodyCLN8 Reaktivität: Human, Hund WB Wirt: Kaninchen Polyclonal unconjugated
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Applikationshinweise
- WB,1:500 - 1:2000,IHC,1:50 - 1:300
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Beschränkungen
- Nur für Forschungszwecke einsetzbar
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Format
- Liquid
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Buffer
- PBS with 0.02 % sodium azide,50 % glycerol, pH 7.3.
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Konservierungsmittel
- Sodium azide
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Vorsichtsmaßnahmen
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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Lagerung
- -20 °C
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Informationen zur Lagerung
- Store at -20°C. Avoid freeze / thaw cycles.
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- CLN8 (Ceroid-Lipofuscinosis, Neuronal 8 (Epilepsy, Progressive with Mental Retardation) (CLN8))
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Andere Bezeichnung
- CLN8
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Hintergrund
- This gene encodes a transmembrane protein belonging to a family of proteins containing TLC domains, which are postulated to function in lipid synthesis, transport, or sensing. The protein localizes to the endoplasmic reticulum (ER), and may recycle between the ER and ER-Golgi intermediate compartment. Mutations in this gene are associated with progressive epilepsy with mental retardation (EMPR), which is a subtype of neuronal ceroid lipofuscinoses (NCL). Patients with mutations in this gene have altered levels of sphingolipid and phospholipids in the brain.,CLN8,C8orf61,EPMR,Cancer,Signal Transduction,Endocrine & Metabolism,Lipid Metabolism,Neuroscience,Neurodegenerative Diseases,CLN8
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Gen-ID
- 2055
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UniProt
- Q9UBY8
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Pathways
- Regulation of Cell Size, Dicarboxylic Acid Transport
Target
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