CLCN1 Antikörper

Produktnummer ABIN7227934

Der Kaninchen Polyklonal anti-CLCN1 Antikörper wird verwendet zum Nachweis von CLCN1 in Proben von Human, Maus und Ratte. Er wurde validiert für WB und ELISA.

Kurzübersicht für CLCN1 Antikörper (ABIN7227934)

Target: CLCN1 (Chloride Channel 1, Skeletal Muscle (CLCN1))

Reaktivität: Human, Maus, Ratte

Wirt: Kaninchen

Klonalität: Polyklonal

Konjugat: Dieser CLCN1 Antikörper ist unkonjugiert

Applikation: Western Blotting (WB), ELISA

Produktdetails anti-CLCN1 Antikörper

Verwendungszweck: Rabbit Anti-CLCN1 Polyclonal Antibody

Spezifität: The antibody detects endogenous levels of CLCN1 protein

Aufreinigung: The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.

Immunogen: Synthesized peptide derived from part region of human CLCN1 protein

Isotyp: IgG

Anwendungsinformationen

Applikationshinweise: Optimal working dilutions should be determined experimentally by the investigator. Suggested starting dilutions are as follows: WB 1:500-2000,ELISA 1:5000-20000

Beschränkungen: Nur für Forschungszwecke einsetzbar

Handhabung

Format: Liquid

Konzentration: 1 mg/mL

Buffer: PBS, 50 % glycerol, 0.05 % Proclin 300, 0.05 %BSA

Konservierungsmittel: ProClin

Vorsichtsmaßnahmen: This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Lagerung: -20 °C

Informationen zur Lagerung: Stable for one year at -20°C from date of shipment. For maximum recovery of product, centrifuge the original vial after thawing and prior to removing the cap. Aliquot to avoid repeated freezing and thawing.

Haltbarkeit: 12 months

Details zu CLCN1

Target: CLCN1 (Chloride Channel 1, Skeletal Muscle (CLCN1))

Andere Bezeichnung: CLCN1

Hintergrund: Chloride channel protein 1, ClC-1, Chloride channel protein, skeletal muscleCLCN1 (Chloride Voltage-Gated Channel 1) is a Protein Coding gene. Diseases associated with CLCN1 include Myotonia Congenita, Recessive and Myotonia Congenita, Dominant The protein encoded by CLCN1 regulates the electric excitability of the skeletal muscle membrane. Mutations in CLCN1 cause two forms of inherited human muscle disorders: recessive generalized myotonia congenita (Becker) and dominant myotonia (Thomsen). Alternative splicing results in multiple transcript variants.

Molekulargewicht: 108kD

Gen-ID: 1180

UniProt: P35523