GCH1 Antikörper
Kurzübersicht für GCH1 Antikörper (ABIN7190766)
Target
Alle GCH1 Antikörper anzeigenReaktivität
Wirt
Klonalität
Konjugat
Applikation
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Kreuzreaktivität
- Human
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Aufreinigung
- Antigen affinity purification
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Immunogen
- Synthetic peptide of Human GCH1
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Isotyp
- IgG
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anti-GTP Cyclohydrolase 1 (GCH1) (AA 84-172) antibody
GCH1 Reaktivität: Human WB, ELISA, IHC (p), IP Wirt: Maus Monoclonal 4A12 unconjugated
anti-GTP Cyclohydrolase 1 (GCH1) (Internal Region) antibodyVerified GCH1 Reaktivität: Human ELISA, IHC Wirt: Ziege Polyclonal unconjugated
anti-GTP Cyclohydrolase 1 (GCH1) (AA 39-67), (N-Term) antibodyGCH1 Reaktivität: Human WB, IHC (p) Wirt: Kaninchen Polyclonal RB21067 unconjugated
anti-GTP Cyclohydrolase 1 (GCH1) (AA 1-250) antibodyGCH1 Reaktivität: Human ELISA, IF Wirt: Maus Monoclonal 1F5 unconjugated
anti-GTP Cyclohydrolase 1 (GCH1) (AA 1-250) antibodyGCH1 Reaktivität: Human ELISA, IF Wirt: Maus Monoclonal 2C4 unconjugated
anti-GTP Cyclohydrolase 1 (GCH1) (AA 1-250) antibodyGCH1 Reaktivität: Human WB, IF Wirt: Maus Polyclonal unconjugated
anti-GTP Cyclohydrolase 1 (GCH1) (AA 34-110) antibodyGCH1 Reaktivität: Maus WB, ELISA, IF (cc), IF (p), IHC (p), IHC (fro) Wirt: Kaninchen Polyclonal unconjugated
anti-GTP Cyclohydrolase 1 (GCH1) (AA 1-250) antibodyGCH1 Reaktivität: Human WB, ELISA Wirt: Maus Polyclonal unconjugated
anti-GTP Cyclohydrolase 1 (GCH1) (AA 84-172) antibodyGCH1 Reaktivität: Human WB, ELISA Wirt: Maus Polyclonal unconjugated
anti-GTP Cyclohydrolase 1 (GCH1) (C-Term) antibodyGCH1 Reaktivität: Human, Maus, Ratte, Rind (Kuh), Hund, Kaninchen, Meerschweinchen, Pferd, Schwein, Fledermaus, Huhn, Hamster, Affe, Xenopus laevis WB Wirt: Kaninchen Polyclonal unconjugated
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Applikationshinweise
- ELISA:1:1000-1:2000, WB:1:200-1:1000, IHC:1:5-1:20,
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Beschränkungen
- Nur für Forschungszwecke einsetzbar
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Format
- Liquid
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Buffer
- -20 °C, pH 7.4 PBS, 0.05 % Sodium azide, 40 % Glycerol
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Konservierungsmittel
- Sodium azide
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Vorsichtsmaßnahmen
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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Lagerung
- -20 °C,-80 °C
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Informationen zur Lagerung
- Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
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- GCH1 (GTP Cyclohydrolase 1 (GCH1))
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Andere Bezeichnung
- GCH1
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Hintergrund
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Background: This gene encodes a member of the GTP cyclohydrolase family. The encoded protein is the first and rate-limiting enzyme in tetrahydrobiopterin (BH4) biosynthesis, catalyzing the conversion of GTP into 7,8-dihydroneopterin triphosphate. BH4 is an essential cofactor required by aromatic amino acid hydroxylases as well as nitric oxide synthases. Mutations in this gene are associated with malignant hyperphenylalaninemia and dopa-responsive dystonia. Several alternatively spliced transcript variants encoding different isoforms have been described, however, not all variants give rise to a functional enzyme.
Aliases: dystonia 14 antibody, DYT 5 antibody, DYT14 antibody, DYT5 antibody, DYT5a antibody, GCH 1 antibody, GCH antibody, Gch1 antibody, GCH1_HUMAN antibody, GTP CH 1 antibody, GTP CH I antibody, GTP cyclohydrolase 1 (dopa responsive dystonia) antibody, GTP cyclohydrolase 1 antibody, GTP cyclohydrolase I antibody, GTP-CH-I antibody, GTPCH 1 antibody, GTPCH1 antibody, Guanosine 5' triphosphate cyclohydrolase I antibody, HPABH4B antibody
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UniProt
- P30793
Target
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