COX6B1 Antikörper (AA 1-86)

Produktnummer ABIN7149179

Dieser Kaninchen Polyklonal Antikörper erkennt spezifisch COX6B1 in ELISA und IF. Er zeigt eine Reaktivität gegenüber Human.

Kurzübersicht für COX6B1 Antikörper (AA 1-86) (ABIN7149179)

Target: COX6B1 (Cytochrome C Oxidase Subunit VIb Polypeptide 1 (Ubiquitous) (COX6B1))

Reaktivität: Human

Wirt: Kaninchen

Klonalität: Polyklonal

Konjugat: Dieser COX6B1 Antikörper ist unkonjugiert

Applikation: ELISA, Immunofluorescence (IF)

Produktdetails anti-COX6B1 Antikörper

Bindungsspezifität: AA 1-86

Verwendungszweck: COX6B1 Antibody

Aufreinigung: Protein G purified

Reinheit: >95 %

Immunogen: Recombinant Human Cytochrome c oxidase subunit 6B1 protein (1-86AA)

Isotyp: IgG

Anwendungsinformationen

Applikationshinweise: Optimal working dilution should be determined by the investigator.

Beschränkungen: Nur für Forschungszwecke einsetzbar

Handhabung

Format: Liquid

Buffer: Preservative: 0.03 % Proclin 300
Constituents: 50 % Glycerol, 0.01M PBS, PH 7.4

Konservierungsmittel: ProClin

Vorsichtsmaßnahmen: This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Lagerung: -20 °C,-80 °C

Informationen zur Lagerung: Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.

Details zu COX6B1

Target: COX6B1 (Cytochrome C Oxidase Subunit VIb Polypeptide 1 (Ubiquitous) (COX6B1))

Andere Bezeichnung: COX6B1

Hintergrund:

Background: Defects in COX6B1 are a cause of mitochondrial complex IV deficiency (MT-C4D) [MIM:220110], also known as cytochrome c oxidase deficiency. A disorder of the mitochondrial respiratory chain with heterogeneous clinical manifestations, ranging from isolated myopathy to severe multisystem disease affecting several tissues and organs. Features include hypertrophic cardiomyopathy, hepatomegaly and liver dysfunction, hypotonia, muscle weakness, excercise intolerance, developmental delay, delayed motor development and mental retardation. A subset of patients manifest Leigh syndrome.

Aliases: COX 6B antibody, COX VIb 1 antibody, COX VIb-1 antibody, COX6B antibody, COX6B1 antibody, COXG antibody, COXVIb1 antibody, CX6B1_HUMAN antibody, Cytochrome c oxidase subunit 6B1 antibody, Cytochrome c oxidase subunit VIb antibody, Cytochrome c oxidase subunit VIb isoform 1 antibody, cytochrome c oxidase subunit VIb polypeptide 1 (ubiquitous) antibody, Cytochrome c oxidase subunit Vib polypeptide 1 antibody

UniProt: P14854