AGA Antikörper
Kurzübersicht für AGA Antikörper (ABIN7128282)
Target
Alle AGA Antikörper anzeigenReaktivität
Wirt
Klonalität
Konjugat
Applikation
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Kreuzreaktivität
- Human, Maus, Ratte
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Aufreinigung
- Antigen affinity purification
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Immunogen
- Fusion protein of Human AGA
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Isotyp
- IgG
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Applikationshinweise
- ELISA:1:1000-1:2000, WB:1:200-1:1000, IHC:1:15-1:50,
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Beschränkungen
- Nur für Forschungszwecke einsetzbar
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Format
- Liquid
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Buffer
- -20 °C, pH 7.4 PBS, 0.05 % Sodium azide, 40 % Glycerol
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Konservierungsmittel
- Sodium azide
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Vorsichtsmaßnahmen
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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Lagerung
- -20 °C,-80 °C
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Informationen zur Lagerung
- Upon receipt, store at -20°C or -80°C. Avoid repeated freeze.
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- AGA (Aspartylglucosaminidase (AGA))
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Andere Bezeichnung
- AGA
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Hintergrund
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Background: Aspartylglucosaminidase is involved in the catabolism of N-linked oligosaccharides of glycoproteins. It cleaves asparagine from N-acetylglucosamines as one of the final steps in the lysosomal breakdown of glycoproteins. The lysosomal storage disease aspartylglycosaminuria is caused by a deficiency in the AGA enzyme. Alternatively spliced transcript variants have been identified.
Aliases: Aga antibody, AGU antibody, Aspartylglucosaminidase antibody, Aspartylglucosylamine deaspartylase antibody, Aspartylglycosaminuria antibody, ASPG_HUMAN antibody, ASRG antibody, GA antibody, Glycosylasparaginase antibody, Glycosylasparaginase beta chain antibody, N(4)-(beta-N-acetylglucosaminyl)-L-asparaginase antibody, N4 (N acetyl beta glucosaminyl) L asparagine amidase antibody, N4-(N-acetyl-beta-glucosaminyl)-L-asparagine amidase antibody
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UniProt
- P20933
Target
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