ACOX1 Antikörper (AA 221-320)
Kurzübersicht für ACOX1 Antikörper (AA 221-320) (ABIN708491)
Target
Alle ACOX1 Antikörper anzeigenReaktivität
Wirt
Klonalität
Konjugat
Applikation
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Bindungsspezifität
- AA 221-320
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Homologie
- Human,Mouse,Rat,Sheep,Pig,Rabbit
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Aufreinigung
- Purified by Protein A.
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Immunogen
- KLH conjugated synthetic peptide derived from human ACOX1
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Isotyp
- IgG
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Applikationshinweise
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WB 1:300-5000
ELISA 1:500-1000
IHC-P 1:200-400
IHC-F 1:100-500
IF(IHC-P) 1:50-200
IF(IHC-F) 1:50-200
IF(ICC) 1:50-200 -
Beschränkungen
- Nur für Forschungszwecke einsetzbar
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Format
- Liquid
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Konzentration
- 1 μg/μL
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Buffer
- 0.01M TBS( pH 7.4) with 1 % BSA, 0.02 % Proclin300 and 50 % Glycerol.
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Konservierungsmittel
- ProClin
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Vorsichtsmaßnahmen
- This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE, which should be handled by trained staff only.
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Lagerung
- 4 °C,-20 °C
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Informationen zur Lagerung
- Shipped at 4°C. Store at -20°C for one year. Avoid repeated freeze/thaw cycles.
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Haltbarkeit
- 12 months
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- ACOX1 (Acyl-CoA Oxidase 1, Palmitoyl (ACOX1))
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Andere Bezeichnung
- ACOX1
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Hintergrund
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Synonyms: ACOX1, ACOX1_HUMAN, AOX antibody Palmitoyl CoA oxidase, Palmitoyl-CoA oxidase, Peroxisomal acyl coenzyme A oxidase 1, Peroxisomal acyl-coenzyme A oxidase 1, SCOX, Straight chain acyl CoA oxidase, Straight-chain acyl-CoA oxidase.
Background: Defects in ACOX1 are the cause of adrenoleukodystrophy pseudoneonatal (Pseudo-NALD), also known as peroxisomal acyl-CoA oxidase deficiency. Pseudo-NALD is a peroxisomal single-enzyme disorder. Clinical features include mental retardation, leukodystrophy, seizures, mild hepatomegaly, hearing deficit. Pseudo-NALD is characterized by increased plasma levels of very-long chain fatty cids, due to decreased or absent peroxisome acyl-CoA oxidase activity. Peroxisomes are intact and functioning.
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Gen-ID
- 51
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Pathways
- Regulation of Lipid Metabolism by PPARalpha, Monocarboxylic Acid Catabolic Process
Target
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