BCKDHA Antikörper (Branched Chain Keto Acid Dehydrogenase E1, alpha Polypeptide)

Details for Product anti-BCKDHA Antibody No. ABIN6572016
Antigen
  • wu:fd20d04
  • zgc:110049
  • BCKDE1A
  • MSU
  • MSUD1
  • OVD1A
  • BCKDA
  • E1a
  • 2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial
  • branched chain keto acid dehydrogenase E1, alpha polypeptide
  • 2-oxoisovalerate dehydrogenase alpha subunit (branched-chain alpha-keto acid dehydrogenase E1 component alpha chain) (BCKDH E1-alpha) (BCKDE1A)
  • branched chain ketoacid dehydrogenase E1, alpha polypeptide
  • LOC704978
  • bckdha
  • BCKDHA
  • BckdhA
  • Bckdha
Reaktivität
Human, Maus, Ratte (Rattus)
25
9
9
3
3
2
2
2
2
1
1
1
1
Wirt
Kaninchen
21
4
Klonalität
Polyklonal
Konjugat
Dieser BCKDHA Antikörper ist unkonjugiert
1
1
1
Applikation
Western Blotting (WB)
21
7
4
4
2
2
2
2
1
Optionen
Immunogen Recombinant protein of human BCKDHA
Isotyp IgG
Reinigung Affinity purification
Plasmids, Primers & others Plasmide, Primers & weitere BCKDHA products on genomics-online (e.g. as negative or positive controls)
Antigen
Andere Bezeichnung BCKDHA (BCKDHA Antibody Abstract)
Hintergrund

Synonyms: Branched chain alpha keto acid dehydrogenase E1 component alpha polypeptide, FLJ45695, OVD1A,2 oxoisovalerate dehydrogenase (lipoamide),2 oxoisovalerate dehydrogenase subunit alpha, mitochondrial ,2-oxoisovalerate dehydrogenase subunit alpha, mitochondrial,BCKDE1A,BCKDH E1 alpha,BCKDH E1-alpha,BCKDHA,Branched chain alpha keto acid dehydrogenase E1 component alpha chain,Branched chain keto acid dehydrogenase E1 alpha polypeptide,Branched chain keto acid dehydrogenase E1, alpha polypeptide (maple syrup urine disease),Branched-chain alpha-keto acid dehydrogenase E1 component alpha chain,MSU,MSUD1,ODBA

Background: The branched-chain alpha-keto acid (BCAA) dehydrogenase (BCKD) complex is an innter mitochondrial enzyme complex that catalyzes the second major step in the catabolism of the branched-chain amino acids leucine, isoleucine, and valine. The BCKD complex consists of three catalytic components: a heterotetrameric (alpha2-beta2) branched-chain alpha-keto acid decarboxylase (E1), a dihydrolipoyl transacylase (E2), and a dihydrolipoamide dehydrogenase (E3). This gene encodes the alpha subunit of the decarboxylase (E1) component. Mutations in this gene result in maple syrup urine disease, type IA. Multiple transcript variants encoding different isoforms have been found for this gene.

Molekulargewicht

Observed_MW: 50kDa

Calculated_MW: 50kDa

Gen-ID 593
UniProt P12694
Applikations-hinweise WB 1:500 - 1:2000
Beschränkungen Nur für Forschungszwecke einsetzbar
Konzentration 1 mg/mL
Buffer Buffer: PBS with 0.02 % sodium azide, 50 % glycerol,  pH 7.3.
Konservierungs-mittel Sodium azide
Vorsichtsmaßnahmen This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
Lagerung -20 °C
Informationen zur Lagerung Store at -20°C. Avoid freeze / thaw cycles.
Bilder des Herstellers
Image no. 1 for anti-Branched Chain Keto Acid Dehydrogenase E1, alpha Polypeptide (BCKDHA) antibody (ABIN6572016) Western blot analysis of extracts of various cell lines, using BCKDHA antibody.
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