ETHE1 Antikörper (Ethylmalonic Encephalopathy 1)

Details for Product anti-ETHE1 Antibody No. ABIN6566792
Target
Reaktivität
Human, Maus, Ratte
43
31
4
2
2
2
2
Wirt
Kaninchen
41
2
Klonalität
Polyklonal
Konjugat
Dieser ETHE1 Antikörper ist unkonjugiert
3
2
2
2
1
1
1
1
1
1
1
1
1
1
Applikation
Western Blotting (WB)
26
13
11
10
7
4
2
2
2
Optionen
Immunogen Recombinant protein of human ETHE1
Isotyp IgG
Reinigung Affinity purification
Target
Andere Bezeichnung ETHE1 (ETHE1 Antibody Abstract)
Hintergrund

Synonyms: Ethe1,ETHE1 protein,mitochondrial precursor,ETHE1,ethylmalonic encephalopathy 1,Ethylmalonic encephalopathy protein 1,hepatoma subtracted clone one,Hepatoma subtracted clone one protein,HSCO,mitochondrial,Protein ETHE1,Protein ETHE1 mitochondrial,YF13H12

Background: This gene encodes a member of the metallo beta-lactamase family of iron-containing proteins involved in the mitochondrial sulfide oxidation pathway. The encoded protein catalyzes the oxidation of a persulfide substrate to sulfite. Certain mutations in this gene cause ethylmalonic encephalopathy, an infantile metabolic disorder affecting the brain, gastrointestinal tract and peripheral vessels. Alternative splicing results in multiple transcript variants encoding different isoforms.

Molekulargewicht

Observed_MW: 28kDa

Calculated_MW: 27kDa

Gen-ID 23474
UniProt O95571
Applikations-hinweise WB 1:200 - 1:1000
Beschränkungen Nur für Forschungszwecke einsetzbar
Konzentration 1 mg/mL
Buffer Buffer: PBS with 0.02 % sodium azide, 50 % glycerol,  pH 7.3.
Konservierungs-mittel Sodium azide
Vorsichtsmaßnahmen This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
Lagerung -20 °C
Informationen zur Lagerung Store at -20°C. Avoid freeze / thaw cycles.
Bilder
Image no. 1 for anti-Ethylmalonic Encephalopathy 1 (ETHE1) antibody (ABIN6566792) Western blot analysis of extracts of various cell lines, using ETHE1 antibody.