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P5CS Antikörper (C-Term)
ALDH18A1
Reaktivität: Human, Maus, Ratte, Rind (Kuh), Schwein, Hund
WB, EIA
Wirt: Ziege
Polyclonal
unconjugated
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Target
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P5CS (ALDH18A1)
(Aldehyde Dehydrogenase 18 Family, Member A1 (ALDH18A1))
Bindungsspezifität
Alle Epitope für P5CS Antikörper
C-Term
Reaktivität
Alle Reaktivitäten für P5CS Antikörper
Human, Maus, Ratte, Rind (Kuh), Schwein, Hund
Wirt
Alle Wirte für P5CS Antikörper
Ziege
Klonalität
Alle Klonalitäten für P5CS Antikörper
Polyklonal
Konjugat
Alle Konjugate für P5CS Antikörper
Dieser P5CS Antikörper ist unkonjugiert
Applikation
Alle Applikationen für P5CS Antikörper
Western Blotting (WB), Enzyme Immunoassay (EIA)
Sequenz
C-SEHGSLKYLH
Spezifität
This antibody is expected to recognize both reported isoforms of ALDH18A1 (NP_002851.2, NP_001017423.1).
Kreuzreaktivität (Details)
Species reactivity (expected):Rat, Canine (Dog), Cow, Pig. Species reactivity (tested):Human, Mouse.
Aufreinigung
Ammonium Sulphate Precipitation followed by Antigen Affinity Chromatography using the immunizing peptide.
Immunogen
Peptide with sequence from the C Terminus of the protein sequence according to NP_002851.2, NP_001017423.1. Genename: ALDH18A1
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Discover our top product ALDH18A1 Primärantikörper
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Anwendungsinformationen
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Applikationshinweise
Optimal working dilution should be determined by the investigator.
Beschränkungen
Nur für Forschungszwecke einsetzbar
Handhabung
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Konzentration
0.5 mg/mL
Buffer
Tris saline, pH 7.3 containing 0.02 % Sodium Azide as preservative and 0.5 % BSA as stabilizer.
Konservierungsmittel
Sodium azide
Vorsichtsmaßnahmen
This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
Handhabung
Avoid repeated freezing and thawing.
Lagerung
4 °C/-20 °C
Informationen zur Lagerung
Store the antibody undiluted at 2-8 °C for one month or (in aliquots) at -20 °C for longer.
Details zu P5CS
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Target
P5CS (ALDH18A1)
(Aldehyde Dehydrogenase 18 Family, Member A1 (ALDH18A1))
Andere Bezeichnung
ALDH18A1 (ALDH18A1 Produkte )
Synonyme
ALDH18A1 antikoerper, ARCL3A antikoerper, GSAS antikoerper, P5CS antikoerper, PYCS antikoerper, 2810433K04Rik antikoerper, AI429789 antikoerper, Pycs antikoerper, cb842 antikoerper, cb899 antikoerper, pycs antikoerper, sb:cb881 antikoerper, wu:fa91f10 antikoerper, wu:fi05f11 antikoerper, wu:fi17d12 antikoerper, aldehyde dehydrogenase 18 family member A1 antikoerper, aldehyde dehydrogenase 18 family, member A1 antikoerper, aldehyde dehydrogenase 18 family member A1 L homeolog antikoerper, ALDH18A1 antikoerper, aldh18a1 antikoerper, Aldh18a1 antikoerper, aldh18a1.L antikoerper
Hintergrund
Defects in ALDH18A1 are the cause of mental retardation-joint hypermobility-skin laxity with or without metabolic abnormalities (MRJHSL) [MIM:612652]. Clinical manifestations include microcephaly, progressive neurologic dysfunction, mental retardation, progeroid appearance, joint hypermobility, skin laxity and hyperelasticity, cataracts. Some patients manifest metabolic disturbances such as hyperammonemia, hypoornithinemia, hypocitrullinemia, hypoargininemia and hypoprolinemia.Synonyms: Aldehyde dehydrogenase family 18 member A1, Delta-1-pyrroline-5-carboxylate synthetase, GSAS, P5CS, PYCS
Molekulargewicht
87.3kDa (NP_002851.2).
Gen-ID
5832
NCBI Accession
NP_001017423
UniProt
P54886
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