NAGLU Antikörper (C-Term)

Produktnummer ABIN5517086

Produktdetails anti-NAGLU Antikörper

Target: NAGLU (N-Acetylglucosaminidase, alpha (NAGLU))

Bindungsspezifität: C-Term

Reaktivität: Human

Wirt: Kaninchen

Klonalität: Polyklonal

Konjugat: Dieser NAGLU Antikörper ist unkonjugiert

Applikation: Western Blotting (WB)

Sequenz: LEALVDSVAQ GIPFQQHQFD KNVFQLEQAF VLSKQRYPSQ PRGDTVDLAK

Aufreinigung: Affinity purified

Immunogen: The immunogen is a synthetic peptide directed towards the C terminal region of human NAGLU

Anwendungsinformationen

Applikationshinweise: Optimal working dilution should be determined by the investigator.

Beschränkungen: Nur für Forschungszwecke einsetzbar

Handhabung

Format: Liquid

Buffer: Liquid. Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.

Konservierungsmittel: Sodium azide

Vorsichtsmaßnahmen: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Lagerung: -20 °C

Informationen zur Lagerung: For short term use, store at 2-8°C up to 1 week. For long term storage, store at -20°C in small aliquots to prevent freeze-thaw cycles.

Details zu NAGLU

Target: NAGLU (N-Acetylglucosaminidase, alpha (NAGLU))

Andere Bezeichnung: NAGLU (NAGLU Produkte)

Synonyme: MPS-IIIB antikoerper, MPS3B antikoerper, NAG antikoerper, UFHSD antikoerper, N-acetylglucosaminidase, alpha antikoerper, N-acetyl-alpha-glucosaminidase antikoerper, alpha-N-acetylglucosaminidase (Sanfilippo disease IIIB) antikoerper, naglu antikoerper, NAGLU antikoerper, Naglu antikoerper

Hintergrund: This gene encodes an enzyme that degrades heparan sulfate by hydrolysis of terminal N-acetyl-D-glucosamine residues in N-acetyl-alpha-D-glucosaminides. Defects in this gene are the cause of mucopolysaccharidosis type IIIB (MPS-IIIB), also known as Sanfilippo syndrome B. This disease is characterized by the lysosomal accumulation and urinary excretion of heparan sulfate.

Alias Symbols: NAG, MPS3B, UFHSD, MPS-IIIB

Protein Size: 639

Gen-ID: 4669

NCBI Accession: NM_000263, NP_000254

UniProt: P54802

Pathways: Glycosaminoglycan Metabolic Process