Peroxisomal Bifunctional Enzyme Antikörper (Middle Region)
Kurzübersicht für Peroxisomal Bifunctional Enzyme Antikörper (Middle Region) (ABIN5514454)
Target
Reaktivität
Wirt
Klonalität
Applikation
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Bindungsspezifität
- Middle Region
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Sequenz
- VIAVDSDKNQ LATANKMITS VLEKEASKMQ QSGHPWSGPK PRLTSSVKEL
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Produktmerkmale
- This is a rabbit polyclonal antibody against ECHP. It was validated on Western Blot.
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Aufreinigung
- Affinity purified
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Immunogen
- The immunogen is a synthetic peptide directed towards the middle region of Human ECHP
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Applikationshinweise
- Optimal working dilution should be determined by the investigator.
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Beschränkungen
- Nur für Forschungszwecke einsetzbar
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Format
- Liquid
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Buffer
- Liquid. Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.
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Konservierungsmittel
- Sodium azide
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Vorsichtsmaßnahmen
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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Lagerung
- -20 °C
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Informationen zur Lagerung
- For short term use, store at 2-8°C up to 1 week. For long term storage, store at -20°C in small aliquots to prevent freeze-thaw cycles.
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- Peroxisomal Bifunctional Enzyme (ECHP)
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Andere Bezeichnung
- ECHP
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Hintergrund
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The protein encoded by this gene is a bifunctional enzyme and is one of the four enzymes of the peroxisomal beta-oxidation pathway. The N-terminal region of the encoded protein contains enoyl-CoA hydratase activity while the C-terminal region contains 3-hydroxyacyl-CoA dehydrogenase activity. Defects in this gene are a cause of peroxisomal disorders such as Zellweger syndrome. Two transcript variants encoding different isoforms have been found for this gene.
Alias Symbols: EHHADH, ECHD,
Protein Size: 723 -
Gen-ID
- 1962
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NCBI Accession
- NP_001957
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UniProt
- Q08426
Target
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