Der Kaninchen Polyklonal Anti-Peroxisomal Bifunctional Enzyme-Antikörper wurde für WB validiert. Er ist geeignet, Peroxisomal Bifunctional Enzyme in Proben von Human zu detektieren.
Produktnummer ABIN5514454
Kurzübersicht für Peroxisomal Bifunctional Enzyme Antikörper (Middle Region) (ABIN5514454)
This is a rabbit polyclonal antibody against ECHP. It was validated on Western Blot.
Aufreinigung
Affinity purified
Immunogen
The immunogen is a synthetic peptide directed towards the middle region of Human ECHP
Applikationshinweise
Optimal working dilution should be determined by the investigator.
Beschränkungen
Nur für Forschungszwecke einsetzbar
Format
Liquid
Buffer
Liquid. Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.
Konservierungsmittel
Sodium azide
Vorsichtsmaßnahmen
This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
Lagerung
-20 °C
Informationen zur Lagerung
For short term use, store at 2-8°C up to 1 week. For long term storage, store at -20°C in small aliquots to prevent freeze-thaw cycles.
Target
Peroxisomal Bifunctional Enzyme (ECHP)
Andere Bezeichnung
ECHP
Hintergrund
The protein encoded by this gene is a bifunctional enzyme and is one of the four enzymes of the peroxisomal beta-oxidation pathway. The N-terminal region of the encoded protein contains enoyl-CoA hydratase activity while the C-terminal region contains 3-hydroxyacyl-CoA dehydrogenase activity. Defects in this gene are a cause of peroxisomal disorders such as Zellweger syndrome. Two transcript variants encoding different isoforms have been found for this gene.