IDUA Antikörper (Middle Region)

Produktnummer ABIN2789574

Produktdetails anti-IDUA Antikörper

Target: IDUA (Iduronidase, alpha-L- (IDUA))

Bindungsspezifität: Middle Region

Reaktivität: Human, Maus, Ratte, Meerschweinchen, Pferd, Rind (Kuh), Hund

Wirt: Kaninchen

Klonalität: Polyklonal

Konjugat: Dieser IDUA Antikörper ist unkonjugiert

Applikation: Western Blotting (WB)

Sequenz: MENQLLPGFE LMGSPSGYFT DFDDKQQVFE WKDLVSLLAR RYIGRYGLTH

Homologie: Cow: 86%, Dog: 90%, Guinea Pig: 100%, Horse: 100%, Human: 100%, Mouse: 86%, Rat: 93%

Produktmerkmale: This is a rabbit polyclonal antibody against Idua. It was validated on Western Blot.

Aufreinigung: Affinity Purified

Immunogen: The immunogen is a synthetic peptide directed towards the middle region of mouse IDUA

Anwendungsinformationen

Beschränkungen: Nur für Forschungszwecke einsetzbar

Handhabung

Format: Liquid

Konzentration: 1 mg/mL

Buffer: Liquid. Purified antibody supplied in 1x PBS buffer with 0.09 % (w/v) sodium azide and 2 % sucrose.

Konservierungsmittel: Sodium azide

Vorsichtsmaßnahmen: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Handhabung: Avoid repeat freeze-thaw cycles.

Lagerung: -20 °C

Informationen zur Lagerung: For short term use, store at 2-8°C up to 1 week. For long term storage, store at -20°C in small aliquots to prevent freeze-thaw cycles.

Details zu IDUA

Target: IDUA (Iduronidase, alpha-L- (IDUA))

Andere Bezeichnung: Idua (IDUA Produkte)

Synonyme: IDA antikoerper, MPS1 antikoerper, 6030426D08 antikoerper, alpha-L-iduronidase antikoerper, MGC80842 antikoerper, si:ch211-12e13.9 antikoerper, IDUA antikoerper, iduronidase, alpha-L- antikoerper, iduronidase, alpha-L- L homeolog antikoerper, alpha-L-iduronidase antikoerper, IDUA antikoerper, Idua antikoerper, idua.L antikoerper, idua antikoerper, LOC5564727 antikoerper

Hintergrund: This gene encodes an enzyme that hydrolyzes the terminal alpha-L-iduronic acid residues of two glycosaminoglycans, dermatan sulfate and heparan sulfate. This hydrolysis is required for the lysosomal degradation of these glycosaminoglycans. Mutations in this gene that result in enzymatic deficiency lead to the autosomal recessive disease mucopolysaccharidosis type I (MPS I).
Alias Symbols: IDA, MPS1
Protein Size: 281

Molekulargewicht: 30 kDa

Gen-ID: 3425

NCBI Accession: NM_000203, NP_000194

UniProt: P35475

Pathways: Glycosaminoglycan Metabolic Process