HADH Antikörper (AA 57-314)

Produktnummer ABIN2468091

Dieses Anti-HADH-Antikörper ist ein Huhn Polyklonal-Antikörper zur Detektion von HADH in WB. Geeignet für Human, Maus und Ratte.

Kurzübersicht für HADH Antikörper (AA 57-314) (ABIN2468091)

Target: HADH (Hydroxyacyl-CoA Dehydrogenase (HADH))

Reaktivität: Human, Maus, Ratte

Wirt: Huhn

Klonalität: Polyklonal

Konjugat: Dieser HADH Antikörper ist unkonjugiert

Applikation: Western Blotting (WB)

Produktdetails anti-HADH Antikörper

Bindungsspezifität: AA 57-314

Aufreinigung: Immunoaffinity Purified

Anwendungsinformationen

Applikationshinweise: Short chain 3-hydroxyacyl-CoA dehydrogenase, mitochondrial antibody can be used for the detection of Short chain 3-hydroxyacyl-CoA dehydrogenase, mitochondrial by Western Blot.

Beschränkungen: Nur für Forschungszwecke einsetzbar

Handhabung

Format: Liquid

Konzentration: 1 mg/mL

Buffer: Phosphate-Buffered Saline. No preservatives added.

Konservierungsmittel: Without preservative

Handhabung: As with all antibodies care should be taken to avoid repeated freeze thaw cycles. Antibodies should not be exposed to prolonged high temperatures.

Lagerung: 4 °C/-20 °C

Informationen zur Lagerung: HADHSC antibody can be stored at 4 °C for short term (weeks). Long term storage should be at -20 °C.

Details zu HADH

Target: HADH (Hydroxyacyl-CoA Dehydrogenase (HADH))

Andere Bezeichnung: HADHSC

Hintergrund: FUNCTION: Plays an essential role in the mitochondrial beta-oxidation of short chain fatty acids. Exerts it highest activity toward 3-hydroxybutyryl-CoA.

DISEASE: Defects in HADHSC are the cause of 3-alpha-hydroxyacyl-CoA dehydrogenase deficiency (HAD deficiency) [MIM:609609]. HAD deficiency is a metabolic disorder with various clinical presentations including hypoglycemia, hepatoencephalopathy, myopathy or cardiomyopathy, and in some cases sudden death.

Molekulargewicht: 34.3 kDa (calculated)

Gen-ID: 3033

NCBI Accession: NP_005318

UniProt: Q16836

Pathways: Negative Regulation of Hormone Secretion, Monocarboxylic Acid Catabolic Process