PEX26
Reaktivität: Human
Wirt: Kaninchen
Polyclonal
FITC
Applikationshinweise
Suggested dilutions: Western blotting: 1.500-1.3000 Immunohistochemistry: 1.50-1.500 Immunofluorescence: 1.100-1.200
Beschränkungen
Nur für Forschungszwecke einsetzbar
Format
Liquid
Buffer
0.1 M Tris-buffered saline with 10 % Glycerol (pH 7.0).0.01 % Thimerosal was added as a preservative.
Konservierungsmittel
Thimerosal (Merthiolate)
Vorsichtsmaßnahmen
Biohazard Informations: This product contains thimerosal which is hazardous.
Lagerung
4 °C/-20 °C
Informationen zur Lagerung
Store at -20 °C for long term preservation (recommended). Store at 4 °C for short term use.
Target
PEX26
(Peroxisomal Biogenesis Factor 26 (PEX26))
Andere Bezeichnung
Peroxin 26
Hintergrund
This gene belongs to the peroxin-26 gene family.It is probably required for protein import into peroxisomes.It anchors PEX1 and PEX6 to peroxisome membranes, possibly to form heteromeric AAA ATPase complexes required for the import of proteins into peroxisomes.Defects in this gene are the cause of peroxisome biogenesis disorder complementation group 8 (PBD-CG8).PBD refers to a group of peroxisomal disorders arising from a failure of protein import into the peroxisomal membrane or matrix.The PBD group is comprised of four disorders: Zellweger syndrome (ZWS), neonatal adrenoleukodystrophy (NALD), infantile Refsum disease (IRD), and classical rhizomelic chondrodysplasia punctata (RCDP).Two transcript variants encoding the same protein have been identified for this gene.[provided by RefSeq]