PEX3 Antikörper (AA 12-61)
Kurzübersicht für PEX3 Antikörper (AA 12-61) (ABIN1535149)
Target
Alle PEX3 Antikörper anzeigenReaktivität
Wirt
Klonalität
Konjugat
Applikation
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Bindungsspezifität
- AA 12-61
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Verwendungszweck
- Peroxin 3 Antibody
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Spezifität
- Peroxin 3 Polyclonal Antibody detects endogenous levels of Peroxin 3 protein.
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Aufreinigung
- The antibody was affinity-purified from rabbit antiserum by affinity-chromatography using epitope-specific immunogen.
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Reinheit
- > 95 %
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Immunogen
- The antiserum was produced against synthesized peptide derived from human PEX3. AA range:12-61
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Isotyp
- IgG
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Applikationshinweise
- WB 1:500-2000,IHC 1:50-300, ELISA 2000-20000
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Beschränkungen
- Nur für Forschungszwecke einsetzbar
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Format
- Liquid
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Konzentration
- 1 mg/mL
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Buffer
- Liquid in PBS containing 50 % glycerol, 0.5 % BSA and 0.02 % sodium azide.
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Konservierungsmittel
- Sodium azide
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Vorsichtsmaßnahmen
- This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
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Lagerung
- -20 °C
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Informationen zur Lagerung
- Store at -20°C/1 year
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Haltbarkeit
- 12 months
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- PEX3 (Peroxisomal Biogenesis Factor 3 (PEX3))
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Andere Bezeichnung
- PEX3
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Hintergrund
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Synonyms: PEX3, Peroxisomal biogenesis factor 3, Peroxin-3, Peroxisomal assembly protein PEX3
Background: The product of this gene is involved in peroxisome biosynthesis and integrity. It assembles membrane vesicles before the matrix proteins are translocated. Peroxins (PEXs) are proteins that are essential for the assembly of functional peroxisomes. The peroxisome biogenesis disorders (PBDs) are a group of genetically heterogeneous autosomal recessive, lethal diseases characterized by multiple defects in peroxisome function. The peroxisomal biogenesis disorders are a heterogeneous group with at least 14 complementation groups and with more than 1 phenotype being observed in cases falling into particular complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene are a cause Zellweger syndrome (ZWS). [provided by RefSeq, Oct 20
Gene Name: PEX3
Protein Name: Peroxisomal biogenesis factor 3
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Molekulargewicht
- 42 kDa
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Gen-ID
- 8504
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OMIM
- 214100
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UniProt
- P56589
Target
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