BPGM Antikörper (AbBy Fluor® 350)
Kurzübersicht für BPGM Antikörper (AbBy Fluor® 350) (ABIN1403193)
Target
Alle BPGM Antikörper anzeigenReaktivität
Wirt
Klonalität
Konjugat
Applikation
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                                            Kreuzreaktivität
- Human, Maus, Ratte
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                                            Aufreinigung
- Purified by Protein A.
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                                            Immunogen
- KLH conjugated synthetic peptide derived from human BPGM
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                                            Isotyp
- IgG
 
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    - 
                                            Applikationshinweise
- IF(IHC-P) 1:50-200
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                                            Beschränkungen
- Nur für Forschungszwecke einsetzbar
 
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                                            Format
- Liquid
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                                            Konzentration
- 1 μg/μL
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                                            Buffer
- Aqueous buffered solution containing 0.01M TBS ( pH 7.4) with 1 % BSA, 0.03 % Proclin300 and 50 % Glycerol.
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                                            Konservierungsmittel
- ProClin
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                                            Vorsichtsmaßnahmen
- This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE, which should be handled by trained staff only.
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                                            Lagerung
- -20 °C
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                                            Informationen zur Lagerung
- Store at -20°C. Aliquot into multiple vials to avoid repeated freeze-thaw cycles.
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                                            Haltbarkeit
- 12 months
 
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    - BPGM (2,3-bisphosphoglycerate Mutase (BPGM))
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                                            Andere Bezeichnung
- BPGM
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                                            Hintergrund
- 
                        Synonyms: 2,3-bisphosphoglycerate mutase, 2,3-bisphosphoglycerate synthase, 3-bisphosphoglycerate mutase, 3-bisphosphoglycerate synthase, 3-diphosphoglycerate mutase, Ab2 098, AI323730, AL022789, Bisphosphoglycerate mutase, BPG dependent PGAM, BPG-dependent PGAM , Bpgm, BPGM, C86192, DPGM, Erythrocyte 2,3 bisphosphoglycerate mutase, PMGE_HUMAN, 2,3-bisphosphoglycerate mutase, erythrocyte, erythrocyte, 2 antibody. Background: BPGM (2,3-bisphosphoglycerate mutase) is a 259 amino acid protein that belongs to the phosphoglycerate mutase family and exists as a homodimer that plays a crucial role in the regulation of hemoglobin oxygen. Specifically, BPGM catalyzes the conversion of 3-D-glyceroyl phosphate to 2,3-bisD-glycerate (2,3-BPG), a reaction that is essential for controlling the concentration of 2,3-BPG within the cell. The gene encoding BPGM maps to human chromosome 7, which houses over 1,000 genes and comprises nearly 5 % of the human genome. Defects in some of the genes localized to chromosome 7 have been linked to Osteogenesis imperfecta, Williams-Beuren syndrome, Pendred syndrome, Lissencephaly, Citrullinemia and Shwachman-Diamond syndrome. Involvement in disease:Defects in BPGM are the cause of bisphosphoglycerate mutase deficiency (BPGMD) . A disease characterized by hemolytic anemia, splenomegaly, cholelithiasis and cholecystitis. 
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                                            Gen-ID
- 669
 Target
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