BCKDHB Proteine

Branched-chain keto acid dehydrogenase is a multienzyme complex associated with the inner membrane of mitochondria, and functions in the catabolism of branched-chain amino acids.

Datenqualität
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Typ
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    Protein
Antigen
  • 6
Reaktivität
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  • 1
  • 1
  • 1
Anwendung
  • 5
  • 3
  • 2
  • 2
  • 1
Wirt
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  • 2
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Bindungsspezifität
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Konjugat
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Protein-Typ
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Format
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6 Produkte
Recombinant Protein, Insektenzellen (Quelle), Reinheit >95 % as determined by SDS PAGE, Size Exclusion Chromatography and Western Blot.
ReaktivitätHuman
Applikation Crys, ELISA, SDS, WB
Bestellinformationen Artikelnr. ABIN3084865
$6,570.39
Zzgl. Versandkosten $45.00 und $22.00 Trockeneis
Lieferung in 50 Werktagen
Recombinant Protein, Insektenzellen (Quelle), Reinheit >95 % as determined by SDS PAGE, Size Exclusion Chromatography and Western Blot.
ReaktivitätMaus
Applikation Crys, ELISA, SDS, WB
Bestellinformationen Artikelnr. ABIN3123598
$6,570.39
Zzgl. Versandkosten $45.00 und $22.00 Trockeneis
Lieferung in 50 Werktagen
ReaktivitätHuman
Applikation AA, AP, ELISA, WB
Bestellinformationen Artikelnr. ABIN2752727
$230.67
2 μg
Zzgl. Versandkosten $45.00 und $22.00 Trockeneis
Lieferung in 11 bis 12 Werktagen
Recombinant Protein, HEK-293 Cells (Quelle), Reinheit > 80 % as determined by SDS-PAGE and Coomassie blue staining
ReaktivitätHuman
Applikation AbP, Func, PI, STD
Bestellinformationen Artikelnr. ABIN2715188
$888.80
20 μg
Zzgl. Versandkosten $45.00 und $22.00 Trockeneis
Lieferung in 11 Werktagen
ReaktivitätRatte (Rattus)
Applikation ELISA
Bestellinformationen Artikelnr. ABIN1474395
$2,927.83
1 mg
Zzgl. Versandkosten $45.00
Lieferung in 60 bis 71 Werktagen
ReaktivitätRind (Kuh)
Applikation ELISA
Bestellinformationen Artikelnr. ABIN1459678
$2,927.83
1 mg
Zzgl. Versandkosten $45.00
Lieferung in 60 bis 71 Werktagen
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BCKDHB Protein Überblick

Protein Überblick

Branched-chain keto acid dehydrogenase is a multienzyme complex associated with the inner membrane of mitochondria, and functions in the catabolism of branched-chain amino acids. The complex consists of multiple copies of 3 components: branched-chain alpha-keto acid decarboxylase (E1), lipoamide acyltransferase (E2) and lipoamide dehydrogenase (E3). This gene encodes the E1 beta subunit, and mutations therein have been associated with maple syrup urine disease (MSUD), type 1B, a disease characterized by a maple syrup odor to the urine in addition to mental and physical retardation, and feeding problems. Alternative splicing at this locus results in transcript variants with different 3' non-coding regions, but encoding the same isoform.

Genbezeichner und Symbole assoziert mit BCKDHB

  • branched chain keto acid dehydrogenase E1, beta polypeptide (BCKDHB) Antikörper
  • branched chain keto acid dehydrogenase E1 subunit beta (BCKDHB) Antikörper
  • branched chain keto acid dehydrogenase E1, beta polypeptide (bckdhb) Antikörper
  • branched chain keto acid dehydrogenase E1, beta polypeptide S homeolog (bckdhb.S) Antikörper
  • branched chain keto acid dehydrogenase E1 subunit beta (Bckdhb) Antikörper
  • branched chain ketoacid dehydrogenase E1, beta polypeptide (Bckdhb) Antikörper
  • BCKDHB Antikörper
  • dJ279A18.1 Antikörper
  • E1B Antikörper
  • zgc:158777 Antikörper

Bezeichner auf Proteinebene für BCKDHB

2-oxoisovalerate dehydrogenase subunit beta, mitochondrial , branched chain keto acid dehydrogenase E1, beta polypeptide (maple syrup urine disease) , mitochondrial branched-chain alpha-keto acid dehydrogenase E1-beta subunit , branched chain keto acid dehydrogenase E1, beta polypeptide , branched chain keto acid dehydrogenase E1 beta polypeptide , branched chain keto acid dehydrogenase E1 beta-like , 2-oxoisovalerate dehydrogenase beta subunit , BCKDE1B , BCKDH E1-beta , branched chain keto acid dehydrogenase E1 beta , branched-chain alpha-keto acid dehydrogenase E1 component beta chain , E1b-beta subunit of the branched-chain complex , branched chain alpha-ketoacid dehydrogenase E1-beta subunit

GENE ID SPEZIES
395375 Gallus gallus
462845 Pan troglodytes
474978 Canis lupus familiaris
569980 Danio rerio
100023799 Monodelphis domestica
100065300 Equus caballus
100137712 Xenopus laevis
100142669 Sus scrofa
100173401 Pongo abelii
100353682 Oryctolagus cuniculus
100597493 Nomascus leucogenys
29711 Rattus norvegicus
594 Homo sapiens
282150 Bos taurus
12040 Mus musculus