GNS Antikörper (AA 293-552)

Produktnummer ABIN6141262

Produktdetails anti-GNS Antikörper

Target: GNS (Glucosamine (N-Acetyl)-6-Sulfatase (GNS))

Bindungsspezifität: AA 293-552

Reaktivität: Human

Wirt: Kaninchen

Klonalität: Polyklonal

Konjugat: Dieser GNS Antikörper ist unkonjugiert

Applikation: Western Blotting (WB)

Sequenz: WQTLLSVDDL VEKLVKRLEF TGELNNTYIF YTSDNGYHTG QFSLPIDKRQ LYEFDIKVPL LVRGPGIKPN QTSKMLVANI DLGPTILDIA GYDLNKTQMD GMSLLPILRG ASNLTWRSDV LVEYQGEGRN VTDPTCPSLS PGVSQCFPDC VCEDAYNNTY ACVRTMSALW NLQYCEFDDQ EVFVEVYNLT ADPDQITNIA KTIDPELLGK MNYRLMMLQS CSGPTCRTPG VFDPGYRFDP RLMFSNRGSV RTRRFSKHLL

Kreuzreaktivität: Human, Maus, Ratte

Produktmerkmale: Polyclonal Antibodies

Aufreinigung: Affinity purification

Immunogen: Recombinant fusion protein containing a sequence corresponding to amino acids 293-552 of human GNS (NP_002067.1).

Isotyp: IgG

Anwendungsinformationen

Applikationshinweise: WB,1:500 - 1:2000

Kommentare:

HIGH QUALITY

Beschränkungen: Nur für Forschungszwecke einsetzbar

Handhabung

Format: Liquid

Buffer: PBS with 0.02 % sodium azide,50 % glycerol, pH 7.3.

Konservierungsmittel: Sodium azide

Vorsichtsmaßnahmen: This product contains Sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.

Lagerung: -20 °C

Informationen zur Lagerung: Store at -20°C. Avoid freeze / thaw cycles.

Details zu GNS

Target: GNS (Glucosamine (N-Acetyl)-6-Sulfatase (GNS))

Andere Bezeichnung: GNS (GNS Produkte)

Synonyme: G6S antikoerper, 2610016K11Rik antikoerper, AU042285 antikoerper, C87209 antikoerper, N28088 antikoerper, NV14559 antikoerper, N-acetylglucosamine-6-sulfatase antikoerper, zgc:114066 antikoerper, gns antikoerper, wu:fi20h10 antikoerper, zgc:55370 antikoerper, glucosamine (N-acetyl)-6-sulfatase antikoerper, glucosamine (N-acetyl)-6-sulfatase S homeolog antikoerper, glucosamine (N-acetyl)-6-sulfatase a antikoerper, N-acetylglucosamine-6-sulfatase antikoerper, glucosamine (N-acetyl)-6-sulfatase (Sanfilippo disease IIID), b antikoerper, GNS antikoerper, Gns antikoerper, gns.S antikoerper, gns antikoerper, gnsa antikoerper, CpipJ_CPIJ000745 antikoerper, Sros_7372 antikoerper, VDBG_04409 antikoerper, Halhy_3165 antikoerper, gnsb antikoerper

Hintergrund: The product of this gene is a lysosomal enzyme found in all cells. It is involved in the catabolism of heparin, heparan sulphate, and keratan sulphate. Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder mucopolysaccharidosis type IIID (Sanfilippo D syndrome). Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome.,GNS,G6S,Cancer,Signal Transduction,Cell Biology & Developmental Biology,Ubiquitin,Endocrine & Metabolism,Amino acid metabolism,GNS

Molekulargewicht: 59 kDa/62 kDa

Gen-ID: 2799

UniProt: P15586

Pathways: Glycosaminoglycan Metabolic Process