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OTC Antikörper (AA 51-150)

OTC Reaktivität: Human WB, ELISA Wirt: Kaninchen Polyclonal unconjugated
Produktnummer ABIN720505
  • Target Alle OTC Antikörper anzeigen
    OTC (Ornithine Carbamoyltransferase (OTC))
    Bindungsspezifität
    • 15
    • 11
    • 8
    • 3
    • 2
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    AA 51-150
    Reaktivität
    • 39
    • 32
    • 25
    • 5
    • 4
    • 4
    • 4
    • 3
    • 3
    • 2
    • 2
    • 2
    • 1
    • 1
    • 1
    • 1
    Human
    Wirt
    • 49
    • 8
    Kaninchen
    Klonalität
    • 49
    • 8
    Polyklonal
    Konjugat
    • 28
    • 4
    • 3
    • 3
    • 2
    • 2
    • 2
    • 2
    • 2
    • 2
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    • 1
    Dieser OTC Antikörper ist unkonjugiert
    Applikation
    • 46
    • 18
    • 14
    • 13
    • 13
    • 12
    • 8
    • 4
    • 3
    • 2
    • 1
    • 1
    • 1
    Western Blotting (WB), ELISA
    Kreuzreaktivität
    Human
    Homologie
    Mouse,Rat,Dog,Cow,Pig,Horse
    Aufreinigung
    Purified by Protein A.
    Immunogen
    KLH conjugated synthetic peptide derived from human OTC
    Isotyp
    IgG
    Top Product
    Discover our top product OTC Primärantikörper
  • Applikationshinweise
    WB 1:300-5000
    ELISA 1:500-1000
    Beschränkungen
    Nur für Forschungszwecke einsetzbar
  • Format
    Liquid
    Konzentration
    1 μg/μL
    Buffer
    0.01M TBS( pH 7.4) with 1 % BSA, 0.02 % Proclin300 and 50 % Glycerol.
    Konservierungsmittel
    ProClin
    Vorsichtsmaßnahmen
    This product contains ProClin: a POISONOUS AND HAZARDOUS SUBSTANCE, which should be handled by trained staff only.
    Lagerung
    4 °C,-20 °C
    Informationen zur Lagerung
    Shipped at 4°C. Store at -20°C for one year. Avoid repeated freeze/thaw cycles.
    Haltbarkeit
    12 months
  • Target
    OTC (Ornithine Carbamoyltransferase (OTC))
    Andere Bezeichnung
    OTC (OTC Produkte)
    Synonyme
    OCTD antikoerper, 2810428A13Rik antikoerper, AA589422 antikoerper, AW457381 antikoerper, OCT antikoerper, Plxn2 antikoerper, mKIAA0463 antikoerper, F1B16.13 antikoerper, F1B16_13 antikoerper, ORNITHINE CARBAMOYLTRANSFERASE antikoerper, ornithine carbamoyltransferase antikoerper, BA4351 antikoerper, PSPTO4164 antikoerper, PLXN2 antikoerper, AI265390 antikoerper, Sf antikoerper, spf antikoerper, si:dkey-19h21.3 antikoerper, ornithine carbamoyltransferase antikoerper, plexin A2 antikoerper, ornithine carbamoyltransferase ArgF antikoerper, ornithine transcarbamylase antikoerper, OTC antikoerper, Plxna2 antikoerper, Otc antikoerper, argF antikoerper, argF-2 antikoerper, atpD-2 antikoerper, CNC04300 antikoerper, PLXNA2 antikoerper, otc antikoerper
    Hintergrund

    Synonyms: OCTD, Ornithine carbamoyltransferase, mitochondrial, Ornithine transcarbamylase, OTCase, OTC

    Background: Defects in OTC are the cause of ornithine carbamoyltransferase deficiency (OTCD) [MIM:311250]. OTCD is an X-linked disorder of the urea cycle which causes a form of hyperammonemia. Mutations with no residual enzyme activity are always expressed in hemizygote males by a very severe neonatal hyperammonemic coma that generally proves to be fatal. Heterozygous females are either asymptomatic or express orotic aciduria spontaneously or after protein intake. The disorder is treatable with supplemental dietary arginine and low protein diet. The arbitrary classification of patients into the 'neonatal' group (clinical hyperammonemia in the first few days of life) and 'late' onset (clinical presentation after the neonatal period) has been used to differentiate severe from mild forms.

    Gen-ID
    5009
    UniProt
    P00480
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