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HPS3 Antikörper (C-Term)

HPS3 Reaktivität: Human WB Wirt: Ziege Polyclonal unconjugated
Produktnummer ABIN374450
  • Target Alle HPS3 Antikörper anzeigen
    HPS3 (Hermansky-Pudlak Syndrome 3 (HPS3))
    Bindungsspezifität
    • 8
    • 8
    • 6
    • 2
    • 2
    • 1
    • 1
    C-Term
    Reaktivität
    • 23
    • 3
    • 3
    • 2
    • 2
    • 2
    • 2
    • 2
    • 1
    • 1
    • 1
    Human
    Wirt
    • 21
    • 1
    • 1
    Ziege
    Klonalität
    • 23
    Polyklonal
    Konjugat
    • 13
    • 2
    • 2
    • 2
    • 2
    • 2
    Dieser HPS3 Antikörper ist unkonjugiert
    Applikation
    • 23
    • 15
    • 4
    • 2
    • 2
    • 2
    Western Blotting (WB)
    Sequenz
    PYLLYCSRKK PLT
    Spezifität
    This antibody recognizes HPS3/Cocoa
    Kreuzreaktivität (Details)
    Species reactivity (tested):Human.
    Aufreinigung
    Ammonium Sulphate Precipitation followed by antigen Affinity Chromatography using the immunizing peptide.
    Immunogen
    Peptide from the C Terminus of the protein sequence according to NP_115759
    Top Product
    Discover our top product HPS3 Primärantikörper
  • Applikationshinweise
    Peptide ELISA: > 1/32,000. Western Blot: 1-3 μg/mL. Detects a band of Approx 110 kDa in A431 cell lysate(Predicted Molecular Weight: 114 kDa).
    Other applications not tested.
    Optimal dilutions are dependent on conditions and should be determined by the user.
    Beschränkungen
    Nur für Forschungszwecke einsetzbar
  • Konzentration
    0.5 mg/mL
    Buffer
    Tris saline, pH 7.3 containing 0.02 % Sodium Azide as preservative and 0.5 % BSA as stabilizer.
    Konservierungsmittel
    Sodium azide
    Vorsichtsmaßnahmen
    This product contains sodium azide: a POISONOUS AND HAZARDOUS SUBSTANCE which should be handled by trained staff only.
    Handhabung
    Avoid repeated freezing and thawing.
    Lagerung
    -20 °C
    Informationen zur Lagerung
    Store the antibody (in aliquots) at -20 °C.
  • Target
    HPS3 (Hermansky-Pudlak Syndrome 3 (HPS3))
    Andere Bezeichnung
    HPS3 (HPS3 Produkte)
    Synonyme
    SUTAL antikoerper, HPS3 antikoerper, coa antikoerper, HPS3, biogenesis of lysosomal organelles complex 2 subunit 1 antikoerper, HPS3, biogenesis of lysosomal organelles complex 2 subunit 1 L homeolog antikoerper, Hermansky-Pudlak syndrome 3 antikoerper, HPS3 antikoerper, hps3.L antikoerper, Hps3 antikoerper
    Hintergrund
    HPS3 is involved in early stages of melanosome biogenesis and maturation. Defects in HPS3 are the cause of the cocoa (coa) mutant, and of Hermansky-Pudlak syndrome type 3 (HPS3). HPS3 is an autosomal recessive disorder, characterized by oculocutaneous albinism, bleeding due to platelet storage pool deficiency, and lysosomal storage defects. This syndrome results from defects of diverse cytoplasmic organelles including melanosomes, platelet dense granules and lysosomes. Ceroid storage in the lungs is associated with pulmonary fibrosis, a common cause of premature death in individuals with HPS.Synonyms: Hermansky-Pudlak syndrome 3
    Gen-ID
    84343
    NCBI Accession
    NP_115759
    UniProt
    Q969F9
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