anti-N-Acetylglutamate Synthase (NAGS) Antikörper

The N-acetylglutamate synthase gene encodes a mitochondrial enzyme that catalyzes the formation of N-acetylglutamate (NAG) from glutamate and acetyl coenzyme-A. Zusätzlich bieten wir Ihnen NAGS Proteine (25) und NAGS Kits (2) und viele weitere Produktgruppen zu diesem Protein an.

Alle Antikörper anzeigen Gen GeneID UniProt
NAGS 162417 Q8N159
NAGS 217214 Q8R4H7
NAGS 303563  
Direkt bei antikoerper-online bestellen
  • +1 877 302 8632
  • +1 888 205 9894 (toll-free)
  • Online bestellen
  • orders@antikoerper-online.de

Top anti-NAGS Antikörper auf antikoerper-online.de

Showing 10 out of 16 products:

Katalog Nr. Reaktivität Wirt Konjugat Applikation Bilder Menge Anbieter Lieferzeit Preis Details
Rind (Kuh) Kaninchen Unkonjugiert WB <b>WB Suggested Anti-NAGS Antibody Titration: </b>1.25ug/ml<br><b>Positive Control: </b>HepG2 cell lysate 100 μL Anmelden zum Anzeigen 2 bis 3 Tage
$229.00
Details
Rind (Kuh) Kaninchen Unkonjugiert WB 100 μg Anmelden zum Anzeigen 7 bis 9 Tage
$493.17
Details
Human Kaninchen Unkonjugiert WB NAGS antibody used at 1.25 ug/ml to detect target protein. 100 μg Anmelden zum Anzeigen 2 bis 3 Tage
$388.93
Details
Hund Kaninchen Unkonjugiert ELISA, WB 100 μg Anmelden zum Anzeigen 2 bis 3 Tage
$446.88
Details
Human Kaninchen Unkonjugiert IF, IHC, WB 100 μL Anmelden zum Anzeigen 16 Days
$476.15
Details
Human Kaninchen Unkonjugiert WB Western Blot: NAGS Antibody [NBP1-79444] - HepG2 cell lysate, concentration 1.25ug/ml. 100 μL Anmelden zum Anzeigen 8 bis 11 Tage
$444.19
Details
Human Kaninchen Unkonjugiert ICC, IF Immunocytochemistry/Immunofluorescence: NAGS Antibody  - Staining of human cell line U-2 OS shows localization to mitochondria. 100 μL Anmelden zum Anzeigen 10 bis 13 Tage
$491.63
Details
Human Maus Unkonjugiert ELISA, WB NAGS polyclonal antibody (A01), Lot # 060106JC01 Western Blot analysis of NAGS expression in K-562 . Western Blot detection against Immunogen (36.89 KDa) . 50 μL Anmelden zum Anzeigen 11 bis 12 Tage
$305.71
Details
Human Kaninchen Unkonjugiert WB   50 μL Anmelden zum Anzeigen 7 bis 9 Tage
$463.83
Details
Human Kaninchen Unkonjugiert IF, ELISA, WB   50 μL Anmelden zum Anzeigen 13 bis 16 Tage
$313.50
Details

NAGS Antikörper nach Reaktivität, Anwendung, Klonalität and Konjugat

Attribute Applikationen Wirt Klonalität
Human ,
,

Mouse (Murine)


Rat (Rattus)


Weitere Antikörper gegen NAGS Interaktionspartner

Human N-Acetylglutamate Synthase (NAGS) Interaktionspartner

  1. The specificity of the assay was validated by demonstrating a complete deficiency of NAGS in liver homogenates from Nags -/- mice. CONCLUSION: The novel NAGS enzyme assay reported herein can be used for the diagnosis of inherited NAGS deficiency and may also be of value in the study of secondary hyperammonemia present in various inborn errors of metabolism as well as drug treatment.

  2. Results identified 36 NAGS mutations in NAGSD patients; 61% of which are missense mutations. Phenotypes associated with these mutations in the GNAT domain are more severe than phenotypes of that of amino acid kinase domain. Enzyme activity and stability assays with 12 mutations, together with in silico structural analysis, support the pathogenic role of most NAGSD-associated mutations found.

  3. Data indicate the formation of alternative N-acylglutamates by N-acetylglutamate synthase (NAGS).

  4. Sp1 (zeige PSG1 Antikörper), CREB (zeige CREB1 Antikörper), HNF-1 (zeige HNF1A Antikörper), and NF-Y, known to be responsive to hormones and diet, regulate NAGS transcription

  5. NAGS deficiency in humans leads to hyperammonemia and can be primary, due to mutations in the NAGS gene or secondary due to other mitochondrial aberrations that interfere with the normal function of the same enzyme.

  6. After the human NAGS gene was identified, mutation analysis revealed that the older sibling on NCG therapy was homozygous for a 971G>A (W324X) mutation.

  7. The first mutation in NAGS has been reported in a family with carbamylglutamate responsive hyperammonemia and normal activity of the urea cycle enzymes.

  8. Gene product expressed in E. coli shown to have NAGS enzyme activity. Gene name provisionally was assigned as NAT7.

  9. report two deleterious mutations within the NAGS gene found in two families with infants presenting with acute neonatal disease; finding confirms the genetic origin of NAGS deficiency

  10. first report of mutation analysis in a series of families affected with deficiency of NAGS

Pig (Porcine) N-Acetylglutamate Synthase (NAGS) Interaktionspartner

  1. The intestinal NAGS mRNA levels were lower in 7- to 28-day-old than in 1-day-old pigs. Immunochemical analysis revealed that NAGS protein was localized in enterocytes of the gut (zeige GUSB Antikörper).

Mouse (Murine) N-Acetylglutamate Synthase (NAGS) Interaktionspartner

  1. The specificity of the assay was validated by demonstrating a complete deficiency of NAGS in liver homogenates from Nags -/- mice. CONCLUSION: The novel NAGS enzyme assay reported herein can be used for the diagnosis of inherited NAGS deficiency and may also be of value in the study of secondary hyperammonemia present in various inborn errors of metabolism as well as drug treatment.

  2. Sp1 (zeige SP1 Antikörper), CREB (zeige CREB1 Antikörper), HNF-1 (zeige HNF1A Antikörper), and NF-Y, known to be responsive to hormones and diet, regulate NAGS transcription

  3. Is a mitochondrial enzyme that catalyzes the formation of N-acetylglutamate (NAG (zeige SCN7A Antikörper))

  4. The biochemical properties of purified recombinant human and mouse NAGS-M and NAGS-C were determined in this study with the goal of better understanding the role of the variable domain in NAGS function.

NAGS Antigen-Profil

Protein Überblick

The N-acetylglutamate synthase gene encodes a mitochondrial enzyme that catalyzes the formation of N-acetylglutamate (NAG) from glutamate and acetyl coenzyme-A. NAG is a cofactor of carbamyl phosphate synthetase I (CPSI), the first enzyme of the urea cycle in mammals. This gene may regulate ureagenesis by altering NAG availability and, thereby, CPSI activity. Deficiencies in N-acetylglutamate synthase have been associated with hyperammonemia.

Genbezeichner und Symbole assoziert mit NAGS

  • N-acetylglutamate synthase (argA) Antikörper
  • N-acetylglutamate synthase (ECs3675) Antikörper
  • amino-acid acetyltransferase ArgA (argA) Antikörper
  • N-acetylglutamate synthase (VP2371) Antikörper
  • N-acetylglutamate synthase (Psyr_0254) Antikörper
  • N-acetylglutamate synthase (Sde_0360) Antikörper
  • N-acetylglutamate synthase (NAGS) Antikörper
  • N-acetylglutamate synthase (Nags) Antikörper
  • 1700120E20Rik Antikörper
  • AGAS Antikörper
  • argA Antikörper
  • RGD1565783 Antikörper
  • VF0585 Antikörper

Bezeichner auf Proteinebene für NAGS

N-acetylglutamate synthase , N-acetylglutamate synthase, mitochondrial , amino-acid acetyltransferase , amino-acid N-acetyltransferase

GENE ID SPEZIES
879475 Pseudomonas aeruginosa PAO1
916513 Escherichia coli O157:H7 str. Sakai
957960 Escherichia coli O157:H7 str. EDL933
1109804 Buchnera aphidicola str. APS (Acyrthosiphon pisum)
1171849 Shewanella oneidensis MR-1
1178706 Vibrio vulnificus CMCP6
1189884 Vibrio parahaemolyticus RIMD 2210633
2765021 Yersinia pestis biovar Microtus str. 91001
2955212 Yersinia pseudotuberculosis IP 32953
3090331 Burkholderia mallei ATCC 23344
3181020 Aromatoleum aromaticum EbN1
3277126 Vibrio fischeri ES114
3365730 Pseudomonas syringae pv. syringae B728a
3480313 Pseudomonas protegens Pf-5
3964826 Saccharophagus degradans 2-40
4713614 Yersinia enterocolitica subsp. enterocolitica 8081
8165153 Photorhabdus asymbiotica subsp. asymbiotica ATCC 43949
162417 Homo sapiens
490943 Canis lupus familiaris
100048960 Sus scrofa
538004 Bos taurus
217214 Mus musculus
303563 Rattus norvegicus
Ausgewählte Anbieter für anti-NAGS (NAGS) Antikörper
Haben Sie etwas anderes gesucht?