anti-Dihydrolipoamide Branched Chain Transacylase E2 (DBT) Antikörper

The branched-chain alpha-keto acid dehydrogenase complex (BCKD) is an inner-mitochondrial enzyme complex involved in the breakdown of the branched-chain amino acids isoleucine, leucine, and valine. Zusätzlich bieten wir Ihnen DBT Kits (9) und DBT Proteine (4) und viele weitere Produktgruppen zu diesem Protein an.

Alle Antikörper anzeigen Gen GeneID UniProt
DBT 1629 P11182
DBT 13171 P53395
DBT 29611  
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Top anti-DBT Antikörper auf antikoerper-online.de

Showing 10 out of 29 products:

Katalog Nr. Reaktivität Wirt Konjugat Applikation Bilder Menge Anbieter Lieferzeit Preis Details
Rind (Kuh) Kaninchen Unkonjugiert IHC, WB <b>WB Suggested Anti-DBT Antibody Titration: </b>0.2-1 ug/ml<br><b>ELISA Titer: </b>1:1562500<br><b>Positive Control: </b>HT1080 cell lysate 100 μL Anmelden zum Anzeigen 6 bis 8 Tage
358,51 €
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Rind (Kuh) Kaninchen Unkonjugiert WB 100 μL Anmelden zum Anzeigen 6 bis 8 Tage
358,51 €
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Fledermaus Kaninchen Unkonjugiert IHC (p), WB Human Kidney: Formalin-Fixed, Paraffin-Embedded (FFPE) Human Skin: Formalin-Fixed, Paraffin-Embedded (FFPE) 50 μg Anmelden zum Anzeigen 11 bis 14 Tage
801,43 €
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Human Maus Unkonjugiert FACS, WB HEK293T cells transfected with either RC201998 overexpress plasmid (Red) or empty vector control plasmid (Blue) were immunostained by anti-DBT antibody (ABIN2455792), and then analyzed by flow cytometry. HEK293T cells were transfected with the pCMV6-ENTRY control (Left lane) or pCMV6-ENTRY DBT (Right lane) cDNA for 48 hrs and lysed. Equivalent amounts of cell lysates (5 µg per lane) were separated by SDS-PAGE and immunoblotted with anti-DBT. 100 μL Anmelden zum Anzeigen 6 bis 8 Tage
418,10 €
Details
Human Kaninchen Unkonjugiert ICC, IF, IHC, IHC (p), WB Immunocytochemistry/Immunofluorescence: DBT Antibody [NBP1-31760] - Analysis of methanol-fixed A431, using antibody at 1:200 dilution. Western Blot: DBT Antibody [NBP1-31760] - Sample (30 ug of whole cell lysate) A: H1299 B: Hep G2 10% SDS PAGE; antibody diluted at 1:1000. 0.1 mL Anmelden zum Anzeigen 2 bis 4 Tage
341,00 €
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Human Maus Unkonjugiert WB Western Blot analysis of DBT expression in transfected 293T cell line by DBT MaxPab polyclonal antibody.<br><br>Lane 1: DBT transfected lysate(53.02 KDa).<br>Lane 2: Non-transfected lysate.<br> DBT MaxPab polyclonal antibody. Western Blot analysis of DBT expression in human liver. 50 μg Anmelden zum Anzeigen 7 bis 8 Tage
369,60 €
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Human Maus Unkonjugiert FACS, WB 100 μL Anmelden zum Anzeigen 11 bis 14 Tage
626,83 €
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Human Kaninchen Unkonjugiert IHC, IHC (p), WB Immunohistochemistry-Paraffin: DBT Antibody [NBP1-85963] - Staining of human testis shows strong cytoplasmic positivity in leydig cells. Western Blot: DBT Antibody [NBP1-85963] - Lane 1: Marker [kDa] 250, 130, 95, 72, 55, 36, 28, 17, 10.Lane 2: Negative control (vector only transfected HEK293T lysate).Lane 3: Over-expression lysate (Co-expressed with a C-terminal myc-DDK tag (~3.1 kDa) in mammalian HEK293T cells, LY419653) 0.1 mL Anmelden zum Anzeigen 5 bis 8 Tage
335,00 €
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Human Kaninchen Unkonjugiert ICC, IF, IHC, IHC (p), WB Western Blot: DBT Antibody [NBP1-89522] - Lane 1: NIH-3T3 cell lysate (Mouse embryonic fibroblast cells).Lane 2: NBT-II cell lysate (Rat Wistar bladder tumour cells) Western Blot: DBT Antibody [NBP1-89522] - Lane 1: Marker [kDa] 230, 130, 95, 72, 56, 36, 28, 17, 11.Lane 2: Human cell line RT-4.Lane 3: Human cell line U-251MG sp 0.1 mL Anmelden zum Anzeigen 5 bis 8 Tage
335,00 €
Details
Human Kaninchen Unkonjugiert WB DBT antibody was used for immunohistochemistry at a concentration of 4-8 ug/ml. Magnification is at 400X DBT antibody was used for immunohistochemistry at a concentration of 4-8 ug/ml. Magnification is at 400X 50 μg Anmelden zum Anzeigen 6 bis 8 Tage
460,89 €
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DBT Antikörper nach Reaktivität, Anwendung, Klonalität and Konjugat

Attribute Applikationen Wirt Klonalität
Human
,
,
Mouse (Murine)


Rat (Rattus)


Am meisten referenzierte anti-DBT Antikörper

  1. Human Polyclonal DBT Primary Antibody für WB - ABIN514887 : Johnson, Vidoni, Durigon, Pearce, Rorbach, He, Brea-Calvo, Minczuk, Reyes, Holt, Spinazzola: Amino acid starvation has opposite effects on mitochondrial and cytosolic protein synthesis. in PLoS ONE 2014 (PubMed)

Weitere Antikörper gegen DBT Interaktionspartner

Human Dihydrolipoamide Branched Chain Transacylase E2 (DBT) Interaktionspartner

  1. The novel DBT mutation c.650-651insT was more prevalent than the deleted 4.7-kb heterozygote in the Amis population. The reported 4.7-kb deletion indicating a possible founder mutation may be preserved.

  2. Deletion in DBT gene is associated with maple syrup urine disease.

  3. 4 novel mutations in DBT gene resulting in intermittent maple syrup urine disease in 7 Norwegian patients; pathogenic effect of the mutations is depletion of cellular protein; intermittent form of MSUD appears to be due to residual R301C mutant protein

  4. in our cohort more severe enzyme & clinical phenotypes of variant maple syrup urine disease were mainly associated with specific genotypes in BCKDHA (zeige BCKDHA Antikörper) gene; milder enzyme & clinical phenotypes were associated with specific genotypes in BCKDHB (zeige BCKDHB Antikörper) & DBT genes

  5. 30 Maple syrup urine disease Portuguese patients studied; 17 putative mutations have been identified (6 in BCKDHA (zeige BCKDHA Antikörper), 5 in BCKDHB (zeige BCKDHB Antikörper) and 6 in DBT); 7 of are described for the first time.

  6. Examination of the deletion mutation in the E2 (DBT) gene facilitated early MSUD diagnosis and was beneficial for the determination of the proper course of treatment.

  7. In 37% (12 patients) of a total of 64 alleles, the supposed maple syrup urine disease-causing mutations in Turkish patients were located in the BCKDHA (zeige BCKDHA Antikörper) gene, in 44% (14 patients) in the BCKDHB (zeige BCKDHB Antikörper) gene and in 19% (6 patients) in the DBT gene.

  8. two novel type IB MSUD mutations in Israeli patients, which affect the E1beta (zeige PDHB Antikörper) subunit in the decarboxylase (E1) component of the branched-chain alpha-ketoacid dehydrogenase complex

  9. Mutation in DBT causes a subset of maple syrup urine disease in Ashkenazi Jewish population.

Zebrafish Dihydrolipoamide Branched Chain Transacylase E2 (DBT) Interaktionspartner

  1. que mutant larvae exhibit a progressive locomotor defect that culminates in unusual nose-to-tail compressions and an inability to swim. Peripheral nerve recordings demonstrate abnormal locomotor output to the axial muscles used for swimming.

Cow (Bovine) Dihydrolipoamide Branched Chain Transacylase E2 (DBT) Interaktionspartner

  1. This gating mechanism synchronizes the binding of the two substrates to the active-site channel, which serves as a feed-forward switch to coordinate the E2b-catalyzed acyltransfer reaction.

DBT Antigen-Profil

Protein Überblick

The branched-chain alpha-keto acid dehydrogenase complex (BCKD) is an inner-mitochondrial enzyme complex involved in the breakdown of the branched-chain amino acids isoleucine, leucine, and valine. The BCKD complex is thought to be composed of a core of 24 transacylase (E2) subunits, and associated decarboxylase (E1), dehydrogenase (E3), and regulatory subunits. This gene encodes the transacylase (E2) subunit. Mutations in this gene result in maple syrup urine disease, type 2. Alternatively spliced transcript variants have been described, but their biological validity has not been determined.

Genbezeichner und Symbole assoziert mit DBT

  • dihydrolipoamide branched chain transacylase E2 (DBT) Antikörper
  • dihydrolipoamide branched chain transacylase E2 (dbt) Antikörper
  • dihydrolipoamide branched chain transacylase E2 (CpipJ_CPIJ006326) Antikörper
  • dihydrolipoamide branched chain transacylase E2 (BDBG_05874) Antikörper
  • dihydrolipoamide branched chain transacylase E2 (NAEGRDRAFT_78509) Antikörper
  • dihydrolipoamide branched chain transacylase E2 (VDBG_04820) Antikörper
  • dihydrolipoamide branched chain transacylase E2 (PGTG_17722) Antikörper
  • dihydrolipoamide branched chain transacylase E2 (Dbt) Antikörper
  • BCATE2 Antikörper
  • BCKAD-E2 Antikörper
  • BCKADE2 Antikörper
  • D3Wsu60e Antikörper
  • E2 Antikörper
  • E2b Antikörper
  • im:7147214 Antikörper
  • zgc:103768 Antikörper

Bezeichner auf Proteinebene für DBT

lipoamide acyltransferase component of branched-chain alpha-keto acid dehydrogenase complex, mitochondrial , dihydrolipoamide branched chain transacylase E2 , BCKAD E2 subunit , E2 component of branched chain alpha-keto acid dehydrogenase complex , branched chain acyltransferase, E2 component , branched-chain alpha-keto acid dehydrogenase complex component E2 , dihydrolipoamide acetyltransferase component of branched-chain alpha-keto acid dehydrogenase complex , dihydrolipoyl transacylase , dihydrolipoyllysine-residue (2-methylpropanoyl)transferase , lipoamide acyltransferase component of mitochondrial branched-chain alpha-keto acid dehydrogenase complex , mitochondrial branched chain alpha-keto acid dehydrogenase transacylase subunit (E2b) , BCKAD E2 , BCKAD-E2 , BCKADE2 , branched-chain alpha-ketoacid dehydrogenase, E2 subunit , part of the BCKAD complex , que , mitochondrial branched-chain alpha-keto acid dihydrolipoyl acyltransferase , component of branched chain keto acid dehydrogenase complex

GENE ID SPEZIES
457056 Pan troglodytes
100174565 Pongo abelii
549717 Xenopus (Silurana) tropicalis
711547 Macaca mulatta
100050317 Equus caballus
100156530 Sus scrofa
100346987 Oryctolagus cuniculus
6038202 Culex quinquefasciatus
8503735 Ajellomyces dermatitidis SLH14081
8862102 Naegleria gruberi strain NEG-M
9530433 Verticillium alfalfae VaMs.102
10529473 Puccinia graminis f. sp. tritici CRL 75-36-700-3
1629 Homo sapiens
13171 Mus musculus
29611 Rattus norvegicus
541388 Danio rerio
447616 Xenopus laevis
395374 Gallus gallus
479929 Canis lupus familiaris
280759 Bos taurus
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